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Marfan Syndrome beyond Aortic Root—Phenotyping Using Cardiovascular Magnetic Resonance Imaging and Clinical Implications

Marfan syndrome (MFS) is an inherited autosomal-dominant connective tissue disorder with multiorgan involvement including musculoskeletal, respiratory, cardiovascular, ocular, and skin manifestations. Life expectancy in patients with MFS is primarily determined by the degree of cardiovascular involv...

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Detalles Bibliográficos
Autores principales:	Nyktari, Evangelia, Drakopoulou, Maria, Rozos, Panagiotis, Loukopoulou, Sofia, Vrachliotis, Thomas, Kourtidou, Soultana, Toutouzas, Konstantinos
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10223153/ https://www.ncbi.nlm.nih.gov/pubmed/37241174 http://dx.doi.org/10.3390/medicina59050942

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