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A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report

We report the rare case of a giant low-grade appendiceal mucinous neoplasm (LAMN), presenting as ileocecal intussusception. An 80-year-old woman presented in the emergency department of our institution with progressively worsening diffuse abdominal pain during the last 24 h. A CT scan revealed a gia...

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Autores principales: Liapis, Stavros C, Perivoliotis, Konstantinos, Psarianos, Kyriakos, Chatzinikolaou, Charito, Moula, Amalia I, Skoufogiannis, Pavlos, Balogiannis, Ioannis, Lytras, Dimitrios
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10224788/
https://www.ncbi.nlm.nih.gov/pubmed/37251252
http://dx.doi.org/10.1093/jscr/rjad273
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author Liapis, Stavros C
Perivoliotis, Konstantinos
Psarianos, Kyriakos
Chatzinikolaou, Charito
Moula, Amalia I
Skoufogiannis, Pavlos
Balogiannis, Ioannis
Lytras, Dimitrios
author_facet Liapis, Stavros C
Perivoliotis, Konstantinos
Psarianos, Kyriakos
Chatzinikolaou, Charito
Moula, Amalia I
Skoufogiannis, Pavlos
Balogiannis, Ioannis
Lytras, Dimitrios
author_sort Liapis, Stavros C
collection PubMed
description We report the rare case of a giant low-grade appendiceal mucinous neoplasm (LAMN), presenting as ileocecal intussusception. An 80-year-old woman presented in the emergency department of our institution with progressively worsening diffuse abdominal pain during the last 24 h. A CT scan revealed a giant abdominal mass (98.7 × 127.3 × 107.6 mm) with air-fluid level and imaging characteristics of ileocecal intussusception. An emergency exploratory laparotomy was performed, and a well-circumscribed cystic mass deriving from the appendix was found. A right hemicolectomy was performed, and the histopathological examination confirmed the diagnosis of LAMN. This report aims to raise awareness among surgeons and radiologists, about LAMNs as a differential diagnosis of right iliac fossa masses presenting as acute abdomen.
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spelling pubmed-102247882023-05-28 A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report Liapis, Stavros C Perivoliotis, Konstantinos Psarianos, Kyriakos Chatzinikolaou, Charito Moula, Amalia I Skoufogiannis, Pavlos Balogiannis, Ioannis Lytras, Dimitrios J Surg Case Rep Case Report We report the rare case of a giant low-grade appendiceal mucinous neoplasm (LAMN), presenting as ileocecal intussusception. An 80-year-old woman presented in the emergency department of our institution with progressively worsening diffuse abdominal pain during the last 24 h. A CT scan revealed a giant abdominal mass (98.7 × 127.3 × 107.6 mm) with air-fluid level and imaging characteristics of ileocecal intussusception. An emergency exploratory laparotomy was performed, and a well-circumscribed cystic mass deriving from the appendix was found. A right hemicolectomy was performed, and the histopathological examination confirmed the diagnosis of LAMN. This report aims to raise awareness among surgeons and radiologists, about LAMNs as a differential diagnosis of right iliac fossa masses presenting as acute abdomen. Oxford University Press 2023-05-27 /pmc/articles/PMC10224788/ /pubmed/37251252 http://dx.doi.org/10.1093/jscr/rjad273 Text en Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2023. https://creativecommons.org/licenses/by/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted reuse, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Liapis, Stavros C
Perivoliotis, Konstantinos
Psarianos, Kyriakos
Chatzinikolaou, Charito
Moula, Amalia I
Skoufogiannis, Pavlos
Balogiannis, Ioannis
Lytras, Dimitrios
A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report
title A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report
title_full A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report
title_fullStr A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report
title_full_unstemmed A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report
title_short A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report
title_sort giant low-grade appendiceal mucinous neoplasm (lamn) presenting as ileocecal intussusception: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10224788/
https://www.ncbi.nlm.nih.gov/pubmed/37251252
http://dx.doi.org/10.1093/jscr/rjad273
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