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Infantile fibromatosis of the mandible- Is radical treatment justified?
Infantile fibromatosis is characterized by proliferation of fibrous soft tissue with a potential of invading the adjacent structures but lacks the ability to metastasize, thus making it a fairly benign lesion with borderline characteristics. The pathology resembles sarcomatous growth, therefore maki...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Wolters Kluwer - Medknow
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10235749/ https://www.ncbi.nlm.nih.gov/pubmed/37273428 http://dx.doi.org/10.4103/njms.njms_71_22 |
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author | Raghani, Manish J. Agarwal, Subham S. Ansari, Hafiz M. N. |
author_facet | Raghani, Manish J. Agarwal, Subham S. Ansari, Hafiz M. N. |
author_sort | Raghani, Manish J. |
collection | PubMed |
description | Infantile fibromatosis is characterized by proliferation of fibrous soft tissue with a potential of invading the adjacent structures but lacks the ability to metastasize, thus making it a fairly benign lesion with borderline characteristics. The pathology resembles sarcomatous growth, therefore making it difficult for the clinician to correctly diagnose. There are two variants of extra-abdominal desmoid juvenile and adult variant depending upon the age group it predominately involves. Fibromatosis is comparatively a rare tumour with unpredictable growth and varying local recurrence rates. The mass usually grows slowly, rapid growth and recurrences being mostly associated with the juvenile forms. The disease may present as single or multifocal lesion with widespread distribution, thus requiring whole body scans to identify any insidious growth elsewhere. Here, we report a case of recurrent juvenile/infantile fibromatosis in a 2-year-old child, conservatively managed without any growth disturbance and signs of recurrence. |
format | Online Article Text |
id | pubmed-10235749 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Wolters Kluwer - Medknow |
record_format | MEDLINE/PubMed |
spelling | pubmed-102357492023-06-03 Infantile fibromatosis of the mandible- Is radical treatment justified? Raghani, Manish J. Agarwal, Subham S. Ansari, Hafiz M. N. Natl J Maxillofac Surg Case Report Infantile fibromatosis is characterized by proliferation of fibrous soft tissue with a potential of invading the adjacent structures but lacks the ability to metastasize, thus making it a fairly benign lesion with borderline characteristics. The pathology resembles sarcomatous growth, therefore making it difficult for the clinician to correctly diagnose. There are two variants of extra-abdominal desmoid juvenile and adult variant depending upon the age group it predominately involves. Fibromatosis is comparatively a rare tumour with unpredictable growth and varying local recurrence rates. The mass usually grows slowly, rapid growth and recurrences being mostly associated with the juvenile forms. The disease may present as single or multifocal lesion with widespread distribution, thus requiring whole body scans to identify any insidious growth elsewhere. Here, we report a case of recurrent juvenile/infantile fibromatosis in a 2-year-old child, conservatively managed without any growth disturbance and signs of recurrence. Wolters Kluwer - Medknow 2023 2023-04-14 /pmc/articles/PMC10235749/ /pubmed/37273428 http://dx.doi.org/10.4103/njms.njms_71_22 Text en Copyright: © 2023 National Journal of Maxillofacial Surgery https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Raghani, Manish J. Agarwal, Subham S. Ansari, Hafiz M. N. Infantile fibromatosis of the mandible- Is radical treatment justified? |
title | Infantile fibromatosis of the mandible- Is radical treatment justified? |
title_full | Infantile fibromatosis of the mandible- Is radical treatment justified? |
title_fullStr | Infantile fibromatosis of the mandible- Is radical treatment justified? |
title_full_unstemmed | Infantile fibromatosis of the mandible- Is radical treatment justified? |
title_short | Infantile fibromatosis of the mandible- Is radical treatment justified? |
title_sort | infantile fibromatosis of the mandible- is radical treatment justified? |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10235749/ https://www.ncbi.nlm.nih.gov/pubmed/37273428 http://dx.doi.org/10.4103/njms.njms_71_22 |
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