Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis

Pulmonary Langerhans cell histiocytosis (PLCH) is an uncommon lung disease that affects young adults aged 20 to 40 years with current or prior history of smoking. The pathologic cell type in PLCH is a dendritic cell of the monocyte-macrophage line that resembles cutaneous Langerhans cells. This repo...

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Detalles Bibliográficos
Autores principales: Patel, Priya, Anamika, FNU, Ali, Rana
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Pulmonology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10237305/
https://www.ncbi.nlm.nih.gov/pubmed/37273350
http://dx.doi.org/10.7759/cureus.38486
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author Patel, Priya
Anamika, FNU
Ali, Rana
author_facet Patel, Priya
Anamika, FNU
Ali, Rana
author_sort Patel, Priya
collection PubMed
description Pulmonary Langerhans cell histiocytosis (PLCH) is an uncommon lung disease that affects young adults aged 20 to 40 years with current or prior history of smoking. The pathologic cell type in PLCH is a dendritic cell of the monocyte-macrophage line that resembles cutaneous Langerhans cells. This report presents the case of a 42-year-old woman with PLCH. We discuss her clinical symptoms, diagnostic tests, and treatment plan, with a specific focus on the radiologic features. The patient exhibited a radiologic appearance similar to that of lymphangiomyomatosis with histologic evidence of PLCH.
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spelling pubmed-102373052023-06-03 Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis Patel, Priya Anamika, FNU Ali, Rana Cureus Pulmonology Pulmonary Langerhans cell histiocytosis (PLCH) is an uncommon lung disease that affects young adults aged 20 to 40 years with current or prior history of smoking. The pathologic cell type in PLCH is a dendritic cell of the monocyte-macrophage line that resembles cutaneous Langerhans cells. This report presents the case of a 42-year-old woman with PLCH. We discuss her clinical symptoms, diagnostic tests, and treatment plan, with a specific focus on the radiologic features. The patient exhibited a radiologic appearance similar to that of lymphangiomyomatosis with histologic evidence of PLCH. Cureus 2023-05-03 /pmc/articles/PMC10237305/ /pubmed/37273350 http://dx.doi.org/10.7759/cureus.38486 Text en Copyright © 2023, Patel et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Pulmonology
Patel, Priya
Anamika, FNU
Ali, Rana
Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis
title Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis
title_full Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis
title_fullStr Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis
title_full_unstemmed Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis
title_short Pulmonary Langerhans Cell Histiocytosis Masquerading as Lymphangioleiomyomatosis
title_sort pulmonary langerhans cell histiocytosis masquerading as lymphangioleiomyomatosis
topic Pulmonology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10237305/
https://www.ncbi.nlm.nih.gov/pubmed/37273350
http://dx.doi.org/10.7759/cureus.38486
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AT anamikafnu pulmonarylangerhanscellhistiocytosismasqueradingaslymphangioleiomyomatosis
AT alirana pulmonarylangerhanscellhistiocytosismasqueradingaslymphangioleiomyomatosis

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