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Combination of triheptanoin with the ketogenic diet in Glucose transporter type 1 deficiency (G1D)

Fuel influx and metabolism replenish carbon lost during normal neural activity. Ketogenic diets studied in epilepsy, dementia and other disorders do not sustain such replenishment because their ketone body derivatives contain four carbon atoms and are thus devoid of this anaplerotic or net carbon do...

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Detalles Bibliográficos
Autores principales:	Avila, Adrian, Málaga, Ignacio, Sirsi, Deepa, Kayani, Saima, Primeaux, Sharon, Kathote, Gauri A., Jakkamsetti, Vikram, Kallem, Raja Reddy, Putnam, William C., Park, Jason Y., Shinnar, Shlomo, Pascual, Juan M.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Nature Publishing Group UK 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10238483/ https://www.ncbi.nlm.nih.gov/pubmed/37268656 http://dx.doi.org/10.1038/s41598-023-36001-x

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