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Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case

Polysplenia syndrome is a rare congenital anomaly characterized by multiple spleens and associated organ anomalies, which can present with serious complications such as splenic infarction. Diagnosis and management of the disorder can be challenging due to the presence of associated anomalies and the...

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Autores principales: Abdullah, Ruya A, Alharbi, Mohammed A, Alnutaifi, Faisal M, Faqih, Abdulrahman I, Alduraibi, Khalid M, Alharbi, Ahlam S
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10239649/
https://www.ncbi.nlm.nih.gov/pubmed/37284391
http://dx.doi.org/10.7759/cureus.38589
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author Abdullah, Ruya A
Alharbi, Mohammed A
Alnutaifi, Faisal M
Faqih, Abdulrahman I
Alduraibi, Khalid M
Alharbi, Ahlam S
author_facet Abdullah, Ruya A
Alharbi, Mohammed A
Alnutaifi, Faisal M
Faqih, Abdulrahman I
Alduraibi, Khalid M
Alharbi, Ahlam S
author_sort Abdullah, Ruya A
collection PubMed
description Polysplenia syndrome is a rare congenital anomaly characterized by multiple spleens and associated organ anomalies, which can present with serious complications such as splenic infarction. Diagnosis and management of the disorder can be challenging due to the presence of associated anomalies and the condition is often diagnosed incidentally. We report a case of a six-year-old girl with no significant medical history who presented to the emergency department with fever, abdominal pain, and vomiting. Physical examination and laboratory investigations showed leukocytosis, anemia, and elevated levels of C-reactive protein. A computed tomography scan revealed splenic infarction with polysplenia syndrome. The patient received intravenous antibiotics and pain management and was closely monitored for complications such as sepsis. Early diagnosis and appropriate management are essential to prevent complications, and close monitoring and follow-up are necessary for long-term management.
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spelling pubmed-102396492023-06-05 Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case Abdullah, Ruya A Alharbi, Mohammed A Alnutaifi, Faisal M Faqih, Abdulrahman I Alduraibi, Khalid M Alharbi, Ahlam S Cureus Emergency Medicine Polysplenia syndrome is a rare congenital anomaly characterized by multiple spleens and associated organ anomalies, which can present with serious complications such as splenic infarction. Diagnosis and management of the disorder can be challenging due to the presence of associated anomalies and the condition is often diagnosed incidentally. We report a case of a six-year-old girl with no significant medical history who presented to the emergency department with fever, abdominal pain, and vomiting. Physical examination and laboratory investigations showed leukocytosis, anemia, and elevated levels of C-reactive protein. A computed tomography scan revealed splenic infarction with polysplenia syndrome. The patient received intravenous antibiotics and pain management and was closely monitored for complications such as sepsis. Early diagnosis and appropriate management are essential to prevent complications, and close monitoring and follow-up are necessary for long-term management. Cureus 2023-05-05 /pmc/articles/PMC10239649/ /pubmed/37284391 http://dx.doi.org/10.7759/cureus.38589 Text en Copyright © 2023, Abdullah et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Emergency Medicine
Abdullah, Ruya A
Alharbi, Mohammed A
Alnutaifi, Faisal M
Faqih, Abdulrahman I
Alduraibi, Khalid M
Alharbi, Ahlam S
Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case
title Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case
title_full Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case
title_fullStr Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case
title_full_unstemmed Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case
title_short Polysplenia Syndrome Complicated by Splenic Infarction: A Report of a Rare Case
title_sort polysplenia syndrome complicated by splenic infarction: a report of a rare case
topic Emergency Medicine
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10239649/
https://www.ncbi.nlm.nih.gov/pubmed/37284391
http://dx.doi.org/10.7759/cureus.38589
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