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A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages
We present a case of autoimmune-acquired factor XIII deficiency associated with systemic lupus erythematosus, which was diagnosed as a cause of repeated intracerebral hemorrhage. An intracerebral hemorrhage occurred in a 24-year-old female patient. Craniotomy was performed to remove the hematoma, bu...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Japan Neurosurgical Society
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10247216/ https://www.ncbi.nlm.nih.gov/pubmed/37293197 http://dx.doi.org/10.2176/jns-nmc.2022-0373 |
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author | OKUMURA, Eitaro ONUKI, Hiroyuki OTSUKA, Kunitoshi SUNAGA, Shigeki TANAKA, Asashi JIMBO, Hiroyuki |
author_facet | OKUMURA, Eitaro ONUKI, Hiroyuki OTSUKA, Kunitoshi SUNAGA, Shigeki TANAKA, Asashi JIMBO, Hiroyuki |
author_sort | OKUMURA, Eitaro |
collection | PubMed |
description | We present a case of autoimmune-acquired factor XIII deficiency associated with systemic lupus erythematosus, which was diagnosed as a cause of repeated intracerebral hemorrhage. An intracerebral hemorrhage occurred in a 24-year-old female patient. Craniotomy was performed to remove the hematoma, but rebleeding occurred at the same site on days 2 and 11, respectively. Detailed blood tests revealed that factor XIII activity decreased. Although autoimmune-acquired factor XIII deficiency is a very rare disease, it can sometimes be fatal when intracerebral hemorrhage occurs. If there is repeated intracerebral hemorrhage, factor XIII activity should be confirmed. |
format | Online Article Text |
id | pubmed-10247216 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | The Japan Neurosurgical Society |
record_format | MEDLINE/PubMed |
spelling | pubmed-102472162023-06-08 A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages OKUMURA, Eitaro ONUKI, Hiroyuki OTSUKA, Kunitoshi SUNAGA, Shigeki TANAKA, Asashi JIMBO, Hiroyuki NMC Case Rep J Case Report We present a case of autoimmune-acquired factor XIII deficiency associated with systemic lupus erythematosus, which was diagnosed as a cause of repeated intracerebral hemorrhage. An intracerebral hemorrhage occurred in a 24-year-old female patient. Craniotomy was performed to remove the hematoma, but rebleeding occurred at the same site on days 2 and 11, respectively. Detailed blood tests revealed that factor XIII activity decreased. Although autoimmune-acquired factor XIII deficiency is a very rare disease, it can sometimes be fatal when intracerebral hemorrhage occurs. If there is repeated intracerebral hemorrhage, factor XIII activity should be confirmed. The Japan Neurosurgical Society 2023-05-17 /pmc/articles/PMC10247216/ /pubmed/37293197 http://dx.doi.org/10.2176/jns-nmc.2022-0373 Text en © 2023 The Japan Neurosurgical Society https://creativecommons.org/licenses/by-nc-nd/4.0/This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives International License. |
spellingShingle | Case Report OKUMURA, Eitaro ONUKI, Hiroyuki OTSUKA, Kunitoshi SUNAGA, Shigeki TANAKA, Asashi JIMBO, Hiroyuki A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages |
title | A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages |
title_full | A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages |
title_fullStr | A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages |
title_full_unstemmed | A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages |
title_short | A Case of Acquired Factor XIII Deficiency with Systemic Lupus Erythematosus Diagnosed after Repeated Intracerebral Hemorrhages |
title_sort | case of acquired factor xiii deficiency with systemic lupus erythematosus diagnosed after repeated intracerebral hemorrhages |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10247216/ https://www.ncbi.nlm.nih.gov/pubmed/37293197 http://dx.doi.org/10.2176/jns-nmc.2022-0373 |
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