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Bickerstaff brainstem encephalitis: A case report

Bickerstaff brainstem encephalitis (BBE) is a rare inflammatory, demyelinating disease that generally has a good prognosis. It's characterized by an acute dysfunction of brainstem occurring few days after an infection. We report the case of an 11-year-old male child with a history of cold, pres...

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Autores principales: Abide, Zakaria, Sif Nasr, Karima, Kaddouri, Soufiane, Edderai, Meryem, Elfenni, Jamal, Salaheddine, Tarik
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10250568/
https://www.ncbi.nlm.nih.gov/pubmed/37304311
http://dx.doi.org/10.1016/j.radcr.2023.04.038
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author Abide, Zakaria
Sif Nasr, Karima
Kaddouri, Soufiane
Edderai, Meryem
Elfenni, Jamal
Salaheddine, Tarik
author_facet Abide, Zakaria
Sif Nasr, Karima
Kaddouri, Soufiane
Edderai, Meryem
Elfenni, Jamal
Salaheddine, Tarik
author_sort Abide, Zakaria
collection PubMed
description Bickerstaff brainstem encephalitis (BBE) is a rare inflammatory, demyelinating disease that generally has a good prognosis. It's characterized by an acute dysfunction of brainstem occurring few days after an infection. We report the case of an 11-year-old male child with a history of cold, presented with ataxia in whom a Bickerstaff encephalitis was attested through brain MRI and who has fully recovered after treatment. The main symptoms are ataxia, ophthalmoplegia, and altered consciousness. CSF analysis and serum antiganglioside antibodies are also very suggestive of the diagnosis that can be suspected clinically and confirmed on brain MRI. The interest of this observation lies in its rarity and on the rapid and spectacular clinical improvement under treatment.
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spelling pubmed-102505682023-06-10 Bickerstaff brainstem encephalitis: A case report Abide, Zakaria Sif Nasr, Karima Kaddouri, Soufiane Edderai, Meryem Elfenni, Jamal Salaheddine, Tarik Radiol Case Rep Case Report Bickerstaff brainstem encephalitis (BBE) is a rare inflammatory, demyelinating disease that generally has a good prognosis. It's characterized by an acute dysfunction of brainstem occurring few days after an infection. We report the case of an 11-year-old male child with a history of cold, presented with ataxia in whom a Bickerstaff encephalitis was attested through brain MRI and who has fully recovered after treatment. The main symptoms are ataxia, ophthalmoplegia, and altered consciousness. CSF analysis and serum antiganglioside antibodies are also very suggestive of the diagnosis that can be suspected clinically and confirmed on brain MRI. The interest of this observation lies in its rarity and on the rapid and spectacular clinical improvement under treatment. Elsevier 2023-06-01 /pmc/articles/PMC10250568/ /pubmed/37304311 http://dx.doi.org/10.1016/j.radcr.2023.04.038 Text en © 2023 The Authors. Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Abide, Zakaria
Sif Nasr, Karima
Kaddouri, Soufiane
Edderai, Meryem
Elfenni, Jamal
Salaheddine, Tarik
Bickerstaff brainstem encephalitis: A case report
title Bickerstaff brainstem encephalitis: A case report
title_full Bickerstaff brainstem encephalitis: A case report
title_fullStr Bickerstaff brainstem encephalitis: A case report
title_full_unstemmed Bickerstaff brainstem encephalitis: A case report
title_short Bickerstaff brainstem encephalitis: A case report
title_sort bickerstaff brainstem encephalitis: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10250568/
https://www.ncbi.nlm.nih.gov/pubmed/37304311
http://dx.doi.org/10.1016/j.radcr.2023.04.038
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