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Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report

Immunoglobulin G4 (IgG4)-related disease is a rare systemic fibroinflammatory condition characterized by organomegaly or tumefactive lesions associated with lymphoplasmacytic infiltration rich in IgG4 plasma cells. We report a case of IgG4-related disease involving the subcutaneous layer of the left...

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Detalles Bibliográficos
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society of Radiology 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10265249/
https://www.ncbi.nlm.nih.gov/pubmed/37324998
http://dx.doi.org/10.3348/jksr.2022.0018
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description Immunoglobulin G4 (IgG4)-related disease is a rare systemic fibroinflammatory condition characterized by organomegaly or tumefactive lesions associated with lymphoplasmacytic infiltration rich in IgG4 plasma cells. We report a case of IgG4-related disease involving the subcutaneous layer of the left upper arm in a 48-year-old female presenting with an unusual soft tissue mass. US and MRI showed an irregular infiltrative soft tissue mass, indicating possible malignancy or inflammation. We discuss the diagnostic criteria, histopathologic features, radiological features, and treatment of IgG4-related disease.
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spelling pubmed-102652492023-06-15 Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report J Korean Soc Radiol Musculoskeletal Imaging Immunoglobulin G4 (IgG4)-related disease is a rare systemic fibroinflammatory condition characterized by organomegaly or tumefactive lesions associated with lymphoplasmacytic infiltration rich in IgG4 plasma cells. We report a case of IgG4-related disease involving the subcutaneous layer of the left upper arm in a 48-year-old female presenting with an unusual soft tissue mass. US and MRI showed an irregular infiltrative soft tissue mass, indicating possible malignancy or inflammation. We discuss the diagnostic criteria, histopathologic features, radiological features, and treatment of IgG4-related disease. The Korean Society of Radiology 2023-05 2023-03-06 /pmc/articles/PMC10265249/ /pubmed/37324998 http://dx.doi.org/10.3348/jksr.2022.0018 Text en Copyrights © 2023 The Korean Society of Radiology https://creativecommons.org/licenses/by-nc/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (https://creativecommons.org/licenses/by-nc/4.0 (https://creativecommons.org/licenses/by-nc/4.0/) ) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Musculoskeletal Imaging
Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report
title Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report
title_full Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report
title_fullStr Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report
title_full_unstemmed Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report
title_short Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Upper Arm: A Case Report
title_sort unusual manifestation of immunoglobulin g4-related disease involving the upper arm: a case report
topic Musculoskeletal Imaging
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10265249/
https://www.ncbi.nlm.nih.gov/pubmed/37324998
http://dx.doi.org/10.3348/jksr.2022.0018
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