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A Case of Pulmonary Alveolar Proteinosis in a 15-Year-Old Female Patient

Pulmonary alveolar proteinosis (PAP) is an extremely rare pulmonary disease that can be classified into primary, secondary, or congenital types. It typically presents with a pattern of interstitial lung disease. This rare condition is even rare in the adolescent or pediatric age group, making this c...

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Detalles Bibliográficos
Autores principales: Khalil, Omar R, Matar, Osama S, Abed Alhaleem, Mohammad H, Attili, Ann A, Ibrahim, Suhib M
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10278061/
https://www.ncbi.nlm.nih.gov/pubmed/37342730
http://dx.doi.org/10.7759/cureus.39254
Descripción
Sumario:Pulmonary alveolar proteinosis (PAP) is an extremely rare pulmonary disease that can be classified into primary, secondary, or congenital types. It typically presents with a pattern of interstitial lung disease. This rare condition is even rare in the adolescent or pediatric age group, making this case particularly rare and interesting. We report a case of a 15-year-old girl who presented with a four-month history of dry cough and exertional dyspnea. After performing a high-resolution computed tomography (HRCT) scan and bronchoalveolar lavage (BAL) with analysis of the BAL fluid, she was eventually diagnosed with PAP. She was then referred to a higher qualified center, where a whole lung lavage (WLL) was performed, resulting in significant improvement of her symptoms.