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Progressive familial intrahepatic cholestasis—outcome and time to transplant after biliary diversion according to genetic subtypes

BACKGROUND: Progressive familial intrahepatic cholestasis (PFIC) is a heterogeneous disease characterized by progressive cholestasis in early childhood. Surgical therapy aims at preventing bile absorption either by external or internal biliary diversion (BD). Several different genetic subtypes encod...

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Detalles Bibliográficos
Autores principales:	Sahloul, Abdulla, Lainka, Elke, Kathemann, Simone, Swoboda, Sandra, Dröge, Carola, Keitel, Verena, Al-Matary, Yahya Saleh, Berger, Michael, Schulze, Maren
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2023
Materias:	Surgery
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10287053/ https://www.ncbi.nlm.nih.gov/pubmed/37361697 http://dx.doi.org/10.3389/fsurg.2023.1074229

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