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Nutrition management of PKU with pegvaliase therapy: update of the web-based PKU nutrition management guideline recommendations

BACKGROUND: The web-based GMDI/SERN PKU Nutrition Management Guideline, published before approval of pegvaliase pharmacotherapy, offers guidance for nutrition management of individuals with phenylketonuria (PKU) treated with dietary therapy and/or sapropterin. An update of this guideline aims to pro...

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Detalles Bibliográficos
Autores principales:	Cunningham, Amy, Rohr, Fran, Splett, Patricia, Mofidi, Shideh, Bausell, Heather, Stembridge, Adrya, Kenneson, Aileen, Singh, Rani H.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2023
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10288765/ https://www.ncbi.nlm.nih.gov/pubmed/37349772 http://dx.doi.org/10.1186/s13023-023-02751-0

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