Cargando…

Approaching hemophagocytic lymphohistiocytosis

Hemophagocytic Lymphohistiocytosis (HLH) is a rare clinical condition characterized by sustained but ineffective immune system activation, leading to severe and systemic hyperinflammation. It may occur as a genetic or sporadic condition, often triggered by an infection. The multifaceted pathogenesis...

Descripción completa

Detalles Bibliográficos
Autores principales:	Chinnici, Aurora, Beneforti, Linda, Pegoraro, Francesco, Trambusti, Irene, Tondo, Annalisa, Favre, Claudio, Coniglio, Maria Luisa, Sieni, Elena
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2023
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10324660/ https://www.ncbi.nlm.nih.gov/pubmed/37426667 http://dx.doi.org/10.3389/fimmu.2023.1210041

Ejemplares similares

S244: OUTCOME OF FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS: REPORT ON 148 PATIENTS FROM THE ITALIAN REGISTRY
por: Pegoraro, Francesco, et al.
Publicado: (2023)

Familial Hemophagocytic Lymphohistiocytosis: When Rare Diseases Shed Light on Immune System Functioning
por: Sieni, Elena, et al.
Publicado: (2014)

Epstein–Barr Virus and Hemophagocytic Lymphohistiocytosis
por: Marsh, Rebecca A.
Publicado: (2018)

Insights into the cellular pathophysiology of familial hemophagocytic lymphohistiocytosis
por: Steen, Erica A., et al.
Publicado: (2023)

Dose-escalating ruxolitinib for refractory hemophagocytic lymphohistiocytosis
por: Song, Yue, et al.
Publicado: (2023)

How Viruses Contribute to the Pathogenesis of Hemophagocytic Lymphohistiocytosis
por: Brisse, Ellen, et al.
Publicado: (2017)

Digenic Inheritance: Evidence and Gaps in Hemophagocytic Lymphohistiocytosis
por: Steen, Erica A., et al.
Publicado: (2021)

Hemophagocytic Lymphohistiocytosis Following COVID-19 Infection
por: Molina, Guarina, et al.
Publicado: (2023)

Use of the JAK Inhibitor Ruxolitinib in the Treatment of Hemophagocytic Lymphohistiocytosis
por: Keenan, Camille, et al.
Publicado: (2021)

Severe COVID-19-Induced Hemophagocytic Lymphohistiocytosis
por: Khan, Shahkar, et al.
Publicado: (2023)

Measles and Secondary Hemophagocytic Lymphohistiocytosis
por: Iaria, Chiara, et al.
Publicado: (2012)

Hemophagocytic Lymphohistiocytosis
por: Kaçar, Ayşe Gonca, et al.
Publicado: (2022)

Mutations of familial hemophagocytic lymphohistiocytosis (FHL) related genes and abnormalities of cytotoxicity function tests in patients with macrophage activation syndrome (MAS) occurring in systemic juvenile idiopathic arthritis (sJIA)
por: Bracaglia, Claudia, et al.
Publicado: (2014)

A predictive model for identifying secondary underlying diseases of hemophagocytic lymphohistiocytosis
por: Gao, Wei-bo, et al.
Publicado: (2023)

Graded Defects in Cytotoxicity Determine Severity of Hemophagocytic Lymphohistiocytosis in Humans and Mice
por: Jessen, Birthe, et al.
Publicado: (2013)

FHLdb: A Comprehensive Database on the Molecular Basis of Familial Hemophagocytic Lymphohistiocytosis
por: Viñas-Giménez, Laura, et al.
Publicado: (2020)

Hemophagocytic Lymphohistiocytosis Associated to Klebsiella pneumoniae Infection: A Case Report
por: Zhang, Zhiyu, et al.
Publicado: (2021)

Genetic predisposition to hemophagocytic lymphohistiocytosis: Report on 500 patients from the Italian registry
por: Cetica, Valentina, et al.
Publicado: (2016)

Simple Evaluation of Clinical Situation and Subtypes of Pediatric Hemophagocytic Lymphohistiocytosis by Cytokine Patterns
por: Xu, Xiao-Jun, et al.
Publicado: (2022)

A prediction model for acute kidney injury in adult patients with hemophagocytic lymphohistiocytosis
por: Wang, Siwen, et al.
Publicado: (2022)

Hemophagocytic lymphohistiocytosis in adults
por: Machaczka, Maciej
Publicado: (2013)

Hemophagocytic lymphohistiocytosis in adults
por: Lee, Hyun Jeong, et al.
Publicado: (2014)

Hemophagocytic Lymphohistiocytosis in Dermatomyositis
por: Liao, Hsien-Tzung, et al.
Publicado: (2019)

Hemophagocytic Lymphohistiocytosis Syndromes
por: Standage, Stephen W., et al.
Publicado: (2014)

Elevated Granzyme B in Cytotoxic Lymphocytes is a Signature of Immune Activation in Hemophagocytic Lymphohistiocytosis
por: Mellor-Heineke, Sabine, et al.
Publicado: (2013)

Pathogenic Gene Mutations or Variants Identified by Targeted Gene Sequencing in Adults With Hemophagocytic Lymphohistiocytosis
por: Miao, Yi, et al.
Publicado: (2019)

Cell Versus Cytokine – Directed Therapies for Hemophagocytic Lymphohistiocytosis (HLH) in Inborn Errors of Immunity
por: Wegehaupt, Oliver, et al.
Publicado: (2020)

The Spectrum of Clinical, Immunological, and Molecular Findings in Familial Hemophagocytic Lymphohistiocytosis: Experience From India
por: Shabrish, Snehal, et al.
Publicado: (2021)

The Outcome of Induction Therapy for EBV-Related Hemophagocytic Lymphohistiocytosis: A Model for Risk Stratification
por: Cui, Tingting, et al.
Publicado: (2022)

Case report: Ruxolitinib as first-line therapy for secondary hemophagocytic lymphohistiocytosis in patients with AIDS
por: Liu, Xiang, et al.
Publicado: (2022)

Case report: Hemophagocytic lymphohistiocytosis in a child with primary immunodeficiency infected with Talaromyces marneffei
por: Yan, Huimin, et al.
Publicado: (2022)

Hepatic sinusoidal hemophagocytosis with and without hemophagocytic lymphohistiocytosis
por: De Gottardi, Jacqueline, et al.
Publicado: (2019)

Two Brothers with Atypical UNC13D-Related Hemophagocytic Lymphohistiocytosis Characterized by Massive Lung and Brain Involvement
por: Giardino, Giuliana, et al.
Publicado: (2017)

Familial Hemophagocytic Lymphohistiocytosis May Present during Adulthood: Clinical and Genetic Features of a Small Series
por: Sieni, Elena, et al.
Publicado: (2012)

Targeted treatment of solid tumors in pediatric precision oncology
por: Bertacca, Ilaria, et al.
Publicado: (2023)

Prognostic value of the albumin-bilirubin score in patients with non-Hodgkin lymphoma-associated hemophagocytic lymphohistiocytosis
por: Cheng, Wanying, et al.
Publicado: (2023)

Monocytes From Patients With Macrophage Activation Syndrome and Secondary Hemophagocytic Lymphohistiocytosis Are Hyperresponsive to Interferon Gamma
por: Pascarella, Antonia, et al.
Publicado: (2021)

Spectrum and trigger identification of hemophagocytic lymphohistiocytosis in adults: A single-center analysis of 555 cases
por: Miao, Yi, et al.
Publicado: (2022)

Case report: Optimized ruxolitinib-based therapy in an infant with familial hemophagocytic lymphohistiocytosis type 3
por: Niizato, Daiki, et al.
Publicado: (2022)

A Rare Case of Hemophagocytic Lymphohistiocytosis in an Adult
por: Behnke, Brian, et al.
Publicado: (2022)

Cannot write session to /tmp/vufind_sessions/sess_3lhcfp56oqmp8bt3jv319l3ck1