Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis

Systemic mastocytosis is a rare myeloproliferative disorder characterized by abnormal accumulation of mast cells in a variety of organs. When affecting the gastrointestinal tracts, it may manifest with steatorrhea, malabsorption, hepatomegaly, splenomegaly, portal hypertension, and ascites, among ot...

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Detalles Bibliográficos
Autores principales: Sarwate, Mrinal, Bakhshwin, Ahmed
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2023
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10328639/
https://www.ncbi.nlm.nih.gov/pubmed/37426569
http://dx.doi.org/10.14309/crj.0000000000001089
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author Sarwate, Mrinal
Bakhshwin, Ahmed
author_facet Sarwate, Mrinal
Bakhshwin, Ahmed
author_sort Sarwate, Mrinal
collection PubMed
description Systemic mastocytosis is a rare myeloproliferative disorder characterized by abnormal accumulation of mast cells in a variety of organs. When affecting the gastrointestinal tracts, it may manifest with steatorrhea, malabsorption, hepatomegaly, splenomegaly, portal hypertension, and ascites, among others. To our knowledge, only one case of systemic mastocytosis has been reported affecting the appendix. We present another case of a 47-year-old woman who was admitted for right-sided acute abdominal pain and found to have systemic mastocytosis in her appendectomy specimen as the first and only manifestation of her disease.
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spelling pubmed-103286392023-07-08 Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis Sarwate, Mrinal Bakhshwin, Ahmed ACG Case Rep J Case Report Systemic mastocytosis is a rare myeloproliferative disorder characterized by abnormal accumulation of mast cells in a variety of organs. When affecting the gastrointestinal tracts, it may manifest with steatorrhea, malabsorption, hepatomegaly, splenomegaly, portal hypertension, and ascites, among others. To our knowledge, only one case of systemic mastocytosis has been reported affecting the appendix. We present another case of a 47-year-old woman who was admitted for right-sided acute abdominal pain and found to have systemic mastocytosis in her appendectomy specimen as the first and only manifestation of her disease. Wolters Kluwer 2023-07-07 /pmc/articles/PMC10328639/ /pubmed/37426569 http://dx.doi.org/10.14309/crj.0000000000001089 Text en © 2023 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (https://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Case Report
Sarwate, Mrinal
Bakhshwin, Ahmed
Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis
title Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis
title_full Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis
title_fullStr Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis
title_full_unstemmed Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis
title_short Acute Appendicitis as the First and the Only Presentation of Systemic Mastocytosis
title_sort acute appendicitis as the first and the only presentation of systemic mastocytosis
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10328639/
https://www.ncbi.nlm.nih.gov/pubmed/37426569
http://dx.doi.org/10.14309/crj.0000000000001089
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