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Hemophagocytic inflammatory syndrome in ADA-SCID: report of two cases and literature review
Hemophagocytic inflammatory syndrome (HIS) is a rare form of secondary hemophagocytic lymphohistiocytosis caused by an impaired equilibrium between natural killer and cytotoxic T-cell activity, evolving in hypercytokinemia and multiorgan failure. In the context of inborn errors of immunity, HIS occu...
Autores principales: | Fratini, Elena Sophia, Migliavacca, Maddalena, Barzaghi, Federica, Fossati, Claudia, Giannelli, Stefania, Monti, Ilaria, Casiraghi, Miriam, Ferrua, Francesca, Recupero, Salvatore, Consiglieri, Giulia, Calbi, Valeria, Tucci, Francesca, Gallo, Vera, Bernardo, Maria Ester, Cenciarelli, Sabina, Palmoni, Monica, Moni, Margherita, Galimberti, Luca, Duse, Marzia, Leonardi, Lucia, Sieni, Elena, Soncini, Elena, Porta, Fulvio, Notarangelo, Lucia Dora, De Santis, Raffaella, Ladogana, Saverio, Aiuti, Alessandro, Cicalese, Maria Pia |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10331599/ https://www.ncbi.nlm.nih.gov/pubmed/37435083 http://dx.doi.org/10.3389/fimmu.2023.1187959 |
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