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Quantitative analysis of mitochondrial morphologies in human induced pluripotent stem cells for Leigh syndrome
Mitochondria are dynamic organelles with wide range of morphologies contributing to regulating different signaling pathways and several cellular functions. Leigh syndrome (LS) is a classic pediatric mitochondrial disorder characterized by complex and variable clinical pathologies, and primarily affe...
Autores principales: | Meshrkey, Fibi, Ayuso, Ana Cabrera, Rao, Raj R., Iyer, Shilpa |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10332439/ https://www.ncbi.nlm.nih.gov/pubmed/34662843 http://dx.doi.org/10.1016/j.scr.2021.102572 |
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