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Longitudinal Analysis of Respiratory Function of Different Types of Limb Girdle Muscular Dystrophies Reveals Independent Trajectories

BACKGROUND AND OBJECTIVES: The prevalence and progression of respiratory muscle dysfunction in patients with limb girdle muscular dystrophies (LGMDs) has been only partially described to date. Most reports include cross-sectional data on a limited number of patients making it difficult to gain a wid...

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Detalles Bibliográficos
Autores principales:	Muni-Lofra, Robert, Juanola-Mayos, Eduard, Schiava, Marianela, Moat, Dionne, Elseed, Maha, Michel-Sodhi, Jassi, Harris, Elizabeth, McCallum, Michelle, Moore, Ursula, Richardson, Mark, Trainor, Christina, Wong, Karen, Malinova, Monika, Bolano-Diaz, Carla, Keogh, Michael John, Ghimenton, Elisabetta, Verdu-Diaz, Jose, Mayhew, Anna, Guglieri, Michela, Straub, Volker, James, Meredith K., Marini-Bettolo, Chiara, Diaz-Manera, Jordi
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Wolters Kluwer 2023
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10335843/ https://www.ncbi.nlm.nih.gov/pubmed/37440793 http://dx.doi.org/10.1212/NXG.0000000000200084

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