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Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report
Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive intermediate soft tissue neoplasm that occurs in the dermis. DFSP generally occurs in young to middle-aged adults and rarely in infancy. Because of its extreme rarity, DFSP is difficult to diagnose and treat, especially when it occurs in...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
S. Karger AG
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10368097/ https://www.ncbi.nlm.nih.gov/pubmed/37497423 http://dx.doi.org/10.1159/000530639 |
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author | Tanaka, Tomoharu Nakayama, Robert Mori, Tomoaki Asano, Naofumi Aramaki-Hattori, Noriko Nakamura, Masaya Matsumoto, Morio |
author_facet | Tanaka, Tomoharu Nakayama, Robert Mori, Tomoaki Asano, Naofumi Aramaki-Hattori, Noriko Nakamura, Masaya Matsumoto, Morio |
author_sort | Tanaka, Tomoharu |
collection | PubMed |
description | Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive intermediate soft tissue neoplasm that occurs in the dermis. DFSP generally occurs in young to middle-aged adults and rarely in infancy. Because of its extreme rarity, DFSP is difficult to diagnose and treat, especially when it occurs in infancy. In this paper, we reported a case of infantile DFSP in which we performed additional wide resection with a 3-cm horizontal margin for a mass that had previously undergone unplanned excision. No tumor recurrence has been seen for 3 years postoperatively. We suggest that the possibility of DFSP should always be considered when an enlarging superficial mass is identified on the trunk, even in an infant. Additionally, radical local treatment is as important for DFSP in infancy as it is for DFSP in adults, even after unplanned excision. |
format | Online Article Text |
id | pubmed-10368097 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | S. Karger AG |
record_format | MEDLINE/PubMed |
spelling | pubmed-103680972023-07-26 Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report Tanaka, Tomoharu Nakayama, Robert Mori, Tomoaki Asano, Naofumi Aramaki-Hattori, Noriko Nakamura, Masaya Matsumoto, Morio Case Rep Oncol Case Report Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive intermediate soft tissue neoplasm that occurs in the dermis. DFSP generally occurs in young to middle-aged adults and rarely in infancy. Because of its extreme rarity, DFSP is difficult to diagnose and treat, especially when it occurs in infancy. In this paper, we reported a case of infantile DFSP in which we performed additional wide resection with a 3-cm horizontal margin for a mass that had previously undergone unplanned excision. No tumor recurrence has been seen for 3 years postoperatively. We suggest that the possibility of DFSP should always be considered when an enlarging superficial mass is identified on the trunk, even in an infant. Additionally, radical local treatment is as important for DFSP in infancy as it is for DFSP in adults, even after unplanned excision. S. Karger AG 2023-07-03 /pmc/articles/PMC10368097/ /pubmed/37497423 http://dx.doi.org/10.1159/000530639 Text en © 2023 The Author(s). Published by S. Karger AG, Basel https://creativecommons.org/licenses/by-nc/4.0/This article is licensed under the Creative Commons Attribution-NonCommercial 4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission. |
spellingShingle | Case Report Tanaka, Tomoharu Nakayama, Robert Mori, Tomoaki Asano, Naofumi Aramaki-Hattori, Noriko Nakamura, Masaya Matsumoto, Morio Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report |
title | Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report |
title_full | Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report |
title_fullStr | Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report |
title_full_unstemmed | Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report |
title_short | Additional Wide Resection of Infantile Dermatofibrosarcoma Protuberans after Unplanned Excision: A Case Report |
title_sort | additional wide resection of infantile dermatofibrosarcoma protuberans after unplanned excision: a case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10368097/ https://www.ncbi.nlm.nih.gov/pubmed/37497423 http://dx.doi.org/10.1159/000530639 |
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