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Rapidly Progressive Portal Cavernoma Cholangiopathy in a Patient With Infeasible Decompressive Shunt Surgery

We present a 27-year-old man with a 2-year history of extrahepatic portal vein obstruction and selective immunoglobulin A deficiency, referred for acute cholangitis from portal cavernoma cholangiopathy (PCC). Because recurrent cholangitis rapidly led to liver failure, orthotopic liver transplantatio...

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Detalles Bibliográficos
Autores principales: Nadinskaia, Maria Yu, Ivashkin, Vladimir T., Nekrasova, Tatiana Р., Novruzbekov, Murad S., Zimina, Larisa N., Kodzoeva, Khava B., Strelkova, Daria A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10371324/
https://www.ncbi.nlm.nih.gov/pubmed/37501936
http://dx.doi.org/10.14309/crj.0000000000000778