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Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report

Ectodermal dysplasia (ED) is an inherited disorder that affects the ectoderm of a developing embryo and impacts structures that originate from it. It typically presents as a triad of missing teeth (anodontia/hypodontia), sparse hair (atrichosis/hypotrichosis), and lack of sweat glands (hypohidrosis)...

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Autores principales: Nejabi, Mohammad Bashir, Anwari, Abdurrahman, Shadab, Hassina, Mtawakel, Nargis, Omarzad, Fariha, Ahmadi, Mohammad Eissa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10416782/
https://www.ncbi.nlm.nih.gov/pubmed/37576744
http://dx.doi.org/10.2147/CCIDE.S419939
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author Nejabi, Mohammad Bashir
Anwari, Abdurrahman
Shadab, Hassina
Mtawakel, Nargis
Omarzad, Fariha
Ahmadi, Mohammad Eissa
author_facet Nejabi, Mohammad Bashir
Anwari, Abdurrahman
Shadab, Hassina
Mtawakel, Nargis
Omarzad, Fariha
Ahmadi, Mohammad Eissa
author_sort Nejabi, Mohammad Bashir
collection PubMed
description Ectodermal dysplasia (ED) is an inherited disorder that affects the ectoderm of a developing embryo and impacts structures that originate from it. It typically presents as a triad of missing teeth (anodontia/hypodontia), sparse hair (atrichosis/hypotrichosis), and lack of sweat glands (hypohidrosis), often accompanied by nail dystrophy and palmoplantar hyperkeratosis. There are two main types of this condition: X-linked anhidrotic or hypohidrotic and hidrotic (autosomal type). The oral manifestation of ED may include anodontia or hypodontia, with or without cleft lip and palate. Tooth loss leads to a decrease in the height of the alveolar ridges, resulting in a reduction of the vertical dimension of the lower face, disappearance of the vermilion border, and prominent lips. As a result, the affected person’s face may resemble that of an elderly individual. The current case report aims to illustrate the prosthodontic rehabilitation of 16-year-old male patient with ectodermal dysplasia and complete anodontia, visiting Dentistry Teaching Hospital, Kabul, Afghanistan. Fortunately, this patient was acceptably managed with the collaboration of several disciplines.
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spelling pubmed-104167822023-08-12 Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report Nejabi, Mohammad Bashir Anwari, Abdurrahman Shadab, Hassina Mtawakel, Nargis Omarzad, Fariha Ahmadi, Mohammad Eissa Clin Cosmet Investig Dent Case Report Ectodermal dysplasia (ED) is an inherited disorder that affects the ectoderm of a developing embryo and impacts structures that originate from it. It typically presents as a triad of missing teeth (anodontia/hypodontia), sparse hair (atrichosis/hypotrichosis), and lack of sweat glands (hypohidrosis), often accompanied by nail dystrophy and palmoplantar hyperkeratosis. There are two main types of this condition: X-linked anhidrotic or hypohidrotic and hidrotic (autosomal type). The oral manifestation of ED may include anodontia or hypodontia, with or without cleft lip and palate. Tooth loss leads to a decrease in the height of the alveolar ridges, resulting in a reduction of the vertical dimension of the lower face, disappearance of the vermilion border, and prominent lips. As a result, the affected person’s face may resemble that of an elderly individual. The current case report aims to illustrate the prosthodontic rehabilitation of 16-year-old male patient with ectodermal dysplasia and complete anodontia, visiting Dentistry Teaching Hospital, Kabul, Afghanistan. Fortunately, this patient was acceptably managed with the collaboration of several disciplines. Dove 2023-08-07 /pmc/articles/PMC10416782/ /pubmed/37576744 http://dx.doi.org/10.2147/CCIDE.S419939 Text en © 2023 Nejabi et al. https://creativecommons.org/licenses/by-nc/3.0/This work is published and licensed by Dove Medical Press Limited. The full terms of this license are available at https://www.dovepress.com/terms.php and incorporate the Creative Commons Attribution – Non Commercial (unported, v3.0) License (http://creativecommons.org/licenses/by-nc/3.0/ (https://creativecommons.org/licenses/by-nc/3.0/) ). By accessing the work you hereby accept the Terms. Non-commercial uses of the work are permitted without any further permission from Dove Medical Press Limited, provided the work is properly attributed. For permission for commercial use of this work, please see paragraphs 4.2 and 5 of our Terms (https://www.dovepress.com/terms.php).
spellingShingle Case Report
Nejabi, Mohammad Bashir
Anwari, Abdurrahman
Shadab, Hassina
Mtawakel, Nargis
Omarzad, Fariha
Ahmadi, Mohammad Eissa
Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
title Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
title_full Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
title_fullStr Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
title_full_unstemmed Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
title_short Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
title_sort prosthodontic management of a patient with ectodermal dysplasia: case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10416782/
https://www.ncbi.nlm.nih.gov/pubmed/37576744
http://dx.doi.org/10.2147/CCIDE.S419939
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