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Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis
Sarcoidosis is a systemic, granulomatous disease of unknown etiology, most often manifested by mediastinal and hilar lymph node enlargement and parenchymal nodules in the lungs. However, it may involve any other organ. Neuro-sarcoidosis, a condition that affects up to 20% of sarcoidosis patients, ca...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10417309/ https://www.ncbi.nlm.nih.gov/pubmed/37568942 http://dx.doi.org/10.3390/diagnostics13152579 |
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author | Zimna, Katarzyna Szturmowicz, Monika Sobiecka, Małgorzata Błasińska, Katarzyna Bartosiewicz, Małgorzata Tomkowski, Witold Z. |
author_facet | Zimna, Katarzyna Szturmowicz, Monika Sobiecka, Małgorzata Błasińska, Katarzyna Bartosiewicz, Małgorzata Tomkowski, Witold Z. |
author_sort | Zimna, Katarzyna |
collection | PubMed |
description | Sarcoidosis is a systemic, granulomatous disease of unknown etiology, most often manifested by mediastinal and hilar lymph node enlargement and parenchymal nodules in the lungs. However, it may involve any other organ. Neuro-sarcoidosis, a condition that affects up to 20% of sarcoidosis patients, can be found in any part of the central or peripheral nervous system and has important ophthalmic and neuro-ophthalmic manifestations. We present two patients with sudden vision loss due to neurosarcoidosis. In both cases, biopsy of the mediastinal lymph node showed non-caseating granulomas consistent with sarcoidosis. Treatment involved high doses of methylprednisolone intravenously, followed by topical dexamethasone eye drops in the first case and a systemic steroid treatment in the second, resulting in symptom relief. Those two cases demonstrate that sarcoidosis should be considered as a differential diagnosis in cases of optic neuritis. |
format | Online Article Text |
id | pubmed-10417309 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-104173092023-08-12 Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis Zimna, Katarzyna Szturmowicz, Monika Sobiecka, Małgorzata Błasińska, Katarzyna Bartosiewicz, Małgorzata Tomkowski, Witold Z. Diagnostics (Basel) Case Report Sarcoidosis is a systemic, granulomatous disease of unknown etiology, most often manifested by mediastinal and hilar lymph node enlargement and parenchymal nodules in the lungs. However, it may involve any other organ. Neuro-sarcoidosis, a condition that affects up to 20% of sarcoidosis patients, can be found in any part of the central or peripheral nervous system and has important ophthalmic and neuro-ophthalmic manifestations. We present two patients with sudden vision loss due to neurosarcoidosis. In both cases, biopsy of the mediastinal lymph node showed non-caseating granulomas consistent with sarcoidosis. Treatment involved high doses of methylprednisolone intravenously, followed by topical dexamethasone eye drops in the first case and a systemic steroid treatment in the second, resulting in symptom relief. Those two cases demonstrate that sarcoidosis should be considered as a differential diagnosis in cases of optic neuritis. MDPI 2023-08-03 /pmc/articles/PMC10417309/ /pubmed/37568942 http://dx.doi.org/10.3390/diagnostics13152579 Text en © 2023 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Case Report Zimna, Katarzyna Szturmowicz, Monika Sobiecka, Małgorzata Błasińska, Katarzyna Bartosiewicz, Małgorzata Tomkowski, Witold Z. Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis |
title | Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis |
title_full | Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis |
title_fullStr | Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis |
title_full_unstemmed | Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis |
title_short | Sudden Vision Loss Due to Optic Neuritis—An Uncommon Presentation of Neurosarcoidosis |
title_sort | sudden vision loss due to optic neuritis—an uncommon presentation of neurosarcoidosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10417309/ https://www.ncbi.nlm.nih.gov/pubmed/37568942 http://dx.doi.org/10.3390/diagnostics13152579 |
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