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Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release

Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-ye...

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Autores principales: Matsuura, Rikako, Shimizu, Yusuke, Matsuura, Naoki, Ntege, Edward Hosea, Wada, Naoki
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10420116/
https://www.ncbi.nlm.nih.gov/pubmed/37568359
http://dx.doi.org/10.3390/jcm12154957
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author Matsuura, Rikako
Shimizu, Yusuke
Matsuura, Naoki
Ntege, Edward Hosea
Wada, Naoki
author_facet Matsuura, Rikako
Shimizu, Yusuke
Matsuura, Naoki
Ntege, Edward Hosea
Wada, Naoki
author_sort Matsuura, Rikako
collection PubMed
description Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-year-old girl with PS manifesting an axillary web containing a fibrous band, which was successfully surgically corrected by a double-opposing Z-plasty. Our surgical approach entailed a meticulous distinction between the deep fibrous band and the superficial cutaneous layer, guided by histopathological findings that indicated the presence of tendon-like tissue, ultimately yielding excellent outcomes. This report will help expand knowledge by highlighting the unique manifestation of PS and emphasizing the importance of employing appropriate treatment approaches. Moreover, addressing both tendon and skin components is essential for optimal contracture release in PS.
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spelling pubmed-104201162023-08-12 Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release Matsuura, Rikako Shimizu, Yusuke Matsuura, Naoki Ntege, Edward Hosea Wada, Naoki J Clin Med Case Report Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-year-old girl with PS manifesting an axillary web containing a fibrous band, which was successfully surgically corrected by a double-opposing Z-plasty. Our surgical approach entailed a meticulous distinction between the deep fibrous band and the superficial cutaneous layer, guided by histopathological findings that indicated the presence of tendon-like tissue, ultimately yielding excellent outcomes. This report will help expand knowledge by highlighting the unique manifestation of PS and emphasizing the importance of employing appropriate treatment approaches. Moreover, addressing both tendon and skin components is essential for optimal contracture release in PS. MDPI 2023-07-28 /pmc/articles/PMC10420116/ /pubmed/37568359 http://dx.doi.org/10.3390/jcm12154957 Text en © 2023 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Matsuura, Rikako
Shimizu, Yusuke
Matsuura, Naoki
Ntege, Edward Hosea
Wada, Naoki
Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
title Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
title_full Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
title_fullStr Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
title_full_unstemmed Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
title_short Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
title_sort management of axillary contracture in poland syndrome: differentiating fibrous band and skin for optimal release
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10420116/
https://www.ncbi.nlm.nih.gov/pubmed/37568359
http://dx.doi.org/10.3390/jcm12154957
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