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Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release
Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-ye...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10420116/ https://www.ncbi.nlm.nih.gov/pubmed/37568359 http://dx.doi.org/10.3390/jcm12154957 |
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author | Matsuura, Rikako Shimizu, Yusuke Matsuura, Naoki Ntege, Edward Hosea Wada, Naoki |
author_facet | Matsuura, Rikako Shimizu, Yusuke Matsuura, Naoki Ntege, Edward Hosea Wada, Naoki |
author_sort | Matsuura, Rikako |
collection | PubMed |
description | Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-year-old girl with PS manifesting an axillary web containing a fibrous band, which was successfully surgically corrected by a double-opposing Z-plasty. Our surgical approach entailed a meticulous distinction between the deep fibrous band and the superficial cutaneous layer, guided by histopathological findings that indicated the presence of tendon-like tissue, ultimately yielding excellent outcomes. This report will help expand knowledge by highlighting the unique manifestation of PS and emphasizing the importance of employing appropriate treatment approaches. Moreover, addressing both tendon and skin components is essential for optimal contracture release in PS. |
format | Online Article Text |
id | pubmed-10420116 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-104201162023-08-12 Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release Matsuura, Rikako Shimizu, Yusuke Matsuura, Naoki Ntege, Edward Hosea Wada, Naoki J Clin Med Case Report Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-year-old girl with PS manifesting an axillary web containing a fibrous band, which was successfully surgically corrected by a double-opposing Z-plasty. Our surgical approach entailed a meticulous distinction between the deep fibrous band and the superficial cutaneous layer, guided by histopathological findings that indicated the presence of tendon-like tissue, ultimately yielding excellent outcomes. This report will help expand knowledge by highlighting the unique manifestation of PS and emphasizing the importance of employing appropriate treatment approaches. Moreover, addressing both tendon and skin components is essential for optimal contracture release in PS. MDPI 2023-07-28 /pmc/articles/PMC10420116/ /pubmed/37568359 http://dx.doi.org/10.3390/jcm12154957 Text en © 2023 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Case Report Matsuura, Rikako Shimizu, Yusuke Matsuura, Naoki Ntege, Edward Hosea Wada, Naoki Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release |
title | Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release |
title_full | Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release |
title_fullStr | Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release |
title_full_unstemmed | Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release |
title_short | Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release |
title_sort | management of axillary contracture in poland syndrome: differentiating fibrous band and skin for optimal release |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10420116/ https://www.ncbi.nlm.nih.gov/pubmed/37568359 http://dx.doi.org/10.3390/jcm12154957 |
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