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Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager

Pachydermodactyly (PDD) is an uncommon and benign digital fibromatosis of unknown etiology. It is characterized by a fusiform swelling of the medial and lateral sides of the fingers, with unspecific histopathological features of an increased number of fibroblasts, collagen, and mucin deposit in the...

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Autores principales: Gallardo-Villamil, Andrea, Cano-Aguilar, Luis E, Pérez-Muñoz, Estela, Rojas-Maruri, Mauricio, Saez de Ocariz, Marimar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10425703/
https://www.ncbi.nlm.nih.gov/pubmed/37588310
http://dx.doi.org/10.7759/cureus.41923
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author Gallardo-Villamil, Andrea
Cano-Aguilar, Luis E
Pérez-Muñoz, Estela
Rojas-Maruri, Mauricio
Saez de Ocariz, Marimar
author_facet Gallardo-Villamil, Andrea
Cano-Aguilar, Luis E
Pérez-Muñoz, Estela
Rojas-Maruri, Mauricio
Saez de Ocariz, Marimar
author_sort Gallardo-Villamil, Andrea
collection PubMed
description Pachydermodactyly (PDD) is an uncommon and benign digital fibromatosis of unknown etiology. It is characterized by a fusiform swelling of the medial and lateral sides of the fingers, with unspecific histopathological features of an increased number of fibroblasts, collagen, and mucin deposit in the dermis. Due to its rarity, PDD could be misdiagnosed as rheumatic arthropathies, which could lead to unnecessary immunosuppressant treatments. Here, we report the case of a 16-year-old boy who presented progressive and asymptomatic soft tissue enlargement of multiple fingers in both hands. The histopathological study and X-ray findings correlated with PDD diagnosis. Intralesional corticoid treatment was indicated with a mild improvement.
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spelling pubmed-104257032023-08-16 Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager Gallardo-Villamil, Andrea Cano-Aguilar, Luis E Pérez-Muñoz, Estela Rojas-Maruri, Mauricio Saez de Ocariz, Marimar Cureus Dermatology Pachydermodactyly (PDD) is an uncommon and benign digital fibromatosis of unknown etiology. It is characterized by a fusiform swelling of the medial and lateral sides of the fingers, with unspecific histopathological features of an increased number of fibroblasts, collagen, and mucin deposit in the dermis. Due to its rarity, PDD could be misdiagnosed as rheumatic arthropathies, which could lead to unnecessary immunosuppressant treatments. Here, we report the case of a 16-year-old boy who presented progressive and asymptomatic soft tissue enlargement of multiple fingers in both hands. The histopathological study and X-ray findings correlated with PDD diagnosis. Intralesional corticoid treatment was indicated with a mild improvement. Cureus 2023-07-15 /pmc/articles/PMC10425703/ /pubmed/37588310 http://dx.doi.org/10.7759/cureus.41923 Text en Copyright © 2023, Gallardo-Villamil et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Dermatology
Gallardo-Villamil, Andrea
Cano-Aguilar, Luis E
Pérez-Muñoz, Estela
Rojas-Maruri, Mauricio
Saez de Ocariz, Marimar
Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager
title Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager
title_full Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager
title_fullStr Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager
title_full_unstemmed Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager
title_short Pachydermodactyly: Soft Tissue Enlargement of the Fingers in a Teenager
title_sort pachydermodactyly: soft tissue enlargement of the fingers in a teenager
topic Dermatology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10425703/
https://www.ncbi.nlm.nih.gov/pubmed/37588310
http://dx.doi.org/10.7759/cureus.41923
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