Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement

ECD is considered to have rapid progression and poor prognosis. Studies have shown that vemurafenib is effective for ECD patients with orbital involvement, but not for ECD with multiple organs. The refinement of treatment approaches and the increased awareness of ECD have led to a dramatic improveme...

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Detalles Bibliográficos
Autores principales: Wang, Xiaomeng, Cao, Jie, Du, Weijiao, Ma, Wenchao, Meng, Bin, Cao, Shui
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10441175/
https://www.ncbi.nlm.nih.gov/pubmed/37609641
http://dx.doi.org/10.1002/ccr3.7780
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author Wang, Xiaomeng
Cao, Jie
Du, Weijiao
Ma, Wenchao
Meng, Bin
Cao, Shui
author_facet Wang, Xiaomeng
Cao, Jie
Du, Weijiao
Ma, Wenchao
Meng, Bin
Cao, Shui
author_sort Wang, Xiaomeng
collection PubMed
description ECD is considered to have rapid progression and poor prognosis. Studies have shown that vemurafenib is effective for ECD patients with orbital involvement, but not for ECD with multiple organs. The refinement of treatment approaches and the increased awareness of ECD have led to a dramatic improvement in prognosis.
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spelling pubmed-104411752023-08-22 Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement Wang, Xiaomeng Cao, Jie Du, Weijiao Ma, Wenchao Meng, Bin Cao, Shui Clin Case Rep Case Report ECD is considered to have rapid progression and poor prognosis. Studies have shown that vemurafenib is effective for ECD patients with orbital involvement, but not for ECD with multiple organs. The refinement of treatment approaches and the increased awareness of ECD have led to a dramatic improvement in prognosis. John Wiley and Sons Inc. 2023-08-21 /pmc/articles/PMC10441175/ /pubmed/37609641 http://dx.doi.org/10.1002/ccr3.7780 Text en © 2023 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by-nc/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc/4.0/ (https://creativecommons.org/licenses/by-nc/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited and is not used for commercial purposes.
spellingShingle Case Report
Wang, Xiaomeng
Cao, Jie
Du, Weijiao
Ma, Wenchao
Meng, Bin
Cao, Shui
Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement
title Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement
title_full Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement
title_fullStr Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement
title_full_unstemmed Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement
title_short Vemurafenib for BRAF V600‐mutant Erdheim–Chester disease presenting with bilateral orbital involvement
title_sort vemurafenib for braf v600‐mutant erdheim–chester disease presenting with bilateral orbital involvement
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10441175/
https://www.ncbi.nlm.nih.gov/pubmed/37609641
http://dx.doi.org/10.1002/ccr3.7780
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