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Phenylalanine Tolerance over Time in Phenylketonuria: A Systematic Review and Meta-Analysis

In phenylketonuria (PKU), natural protein tolerance is defined as the maximum natural protein intake maintaining a blood phenylalanine (Phe) concentration within a target therapeutic range. Tolerance is affected by several factors, and it may differ throughout a person’s lifespan. Data on lifelong P...

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Detalles Bibliográficos
Autores principales:	Pinto, Alex, Ilgaz, Fatma, Evans, Sharon, van Dam, Esther, Rocha, Júlio César, Karabulut, Erdem, Hickson, Mary, Daly, Anne, MacDonald, Anita
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10458574/ https://www.ncbi.nlm.nih.gov/pubmed/37630696 http://dx.doi.org/10.3390/nu15163506

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