Cargando…

Evaluation of a New Glycomacropeptide-Based Protein Substitute in Powdered and Liquid Format in Patients with PKU

(1) Background: Good adherence to a Phe-restricted diet supplemented with an adequate amount of a protein substitute (PS) is important for good clinical outcomes in PKU. Glycomacropeptide (cGMP)-PSs are innovative, palatable alternatives to amino acid-based PSs (AA-PS). This study aimed to evaluate...

Descripción completa

Detalles Bibliográficos
Autores principales:	Delsoglio, Marta, Capener, Rebecca, MacDonald, Anita, Daly, Anne, Ashmore, Catherine, Ellerton, Charlotte, Donald, Sarah, Gaff, Lisa, VanDorp, Louise, Skeath, Rachel, Newby, Camille, Dunning, Georgina, Dale, Clare, Hunjan, Inderdip, White, Lucy, Allen, Heather, Hubbard, Gary P., Stratton, Rebecca J.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10459497/ https://www.ncbi.nlm.nih.gov/pubmed/37630769 http://dx.doi.org/10.3390/nu15163580

Ejemplares similares

Evaluation of a New ‘Mix-In’ Style Glycomacropeptide-Based Protein Substitute for Food and Drinks in Patients with Phenylketonuria and Tyrosinemia
por: Delsoglio, Marta, et al.
Publicado: (2023)

Glycomacropeptide in PKU—Does It Live Up to Its Potential?
por: Daly, Anne, et al.
Publicado: (2022)

Special Low Protein Foods Prescribed in England for PKU Patients: An Analysis of Prescribing Patterns and Cost
por: Wood, Georgina, et al.
Publicado: (2021)

Glycomacropeptide: long-term use and impact on blood phenylalanine, growth and nutritional status in children with PKU
por: Daly, A., et al.
Publicado: (2019)

Growth and Body Composition in PKU Children—A Three-Year Prospective Study Comparing the Effects of L-Amino Acid to Glycomacropeptide Protein Substitutes
por: Daly, Anne, et al.
Publicado: (2021)

Casein Glycomacropeptide: An Alternative Protein Substitute in Tyrosinemia Type I
por: Daly, Anne, et al.
Publicado: (2021)

Protein Substitutes in PKU; Their Historical Evolution
por: Daly, Anne, et al.
Publicado: (2021)

The Impact of the Use of Glycomacropeptide on Satiety and Dietary Intake in Phenylketonuria
por: Daly, Anne, et al.
Publicado: (2020)

The influence of parental food preference and neophobia on children with phenylketonuria (PKU)
por: Evans, Sharon, et al.
Publicado: (2017)

The Effect of Glycomacropeptide versus Amino Acids on Phenylalanine and Tyrosine Variability over 24 Hours in Children with PKU: A Randomized Controlled Trial
por: Daly, Anne, et al.
Publicado: (2019)

How Does Feeding Development and Progression onto Solid Foods in PKU Compare with Non-PKU Children During Weaning?
por: Evans, Sharon, et al.
Publicado: (2019)

Development of national consensus statements on food labelling interpretation and protein allocation in a low phenylalanine diet for PKU
por: Evans, Sharon, et al.
Publicado: (2019)

A Three-Year Longitudinal Study Comparing Bone Mass, Density, and Geometry Measured by DXA, pQCT, and Bone Turnover Markers in Children with PKU Taking L-Amino Acid or Glycomacropeptide Protein Substitutes
por: Daly, Anne, et al.
Publicado: (2021)

Suitability and Allocation of Protein-Containing Foods According to Protein Tolerance in PKU: A 2022 UK National Consensus
por: Gama, Maria Inês, et al.
Publicado: (2022)

The Challenges and Dilemmas of Interpreting Protein Labelling of Prepackaged Foods Encountered by the PKU Community
por: Hall, Imogen, et al.
Publicado: (2022)

Efficacy of a New Low-Protein Multimedia Diet App for PKU
por: Evans, Sharon, et al.
Publicado: (2022)

Hungry for Change: The Experiences of People with PKU, and Their Caregivers, When Eating Out
por: Poole, Grace, et al.
Publicado: (2022)

Mealtime Anxiety and Coping Behaviour in Parents and Children during Weaning in PKU: A Case-Control Study
por: Evans, Sharon, et al.
Publicado: (2019)

Provision and Supervision of Food and Protein Substitute in School for Children with PKU: Parent Experiences
por: Jones, Hannah, et al.
Publicado: (2021)

Protein Labelling Accuracy for UK Patients with PKU Following a Low Protein Diet
por: Kraleva, Dilyana, et al.
Publicado: (2020)

Preliminary Investigation to Review If a Glycomacropeptide Compared to L-Amino Acid Protein Substitute Alters the Pre- and Postprandial Amino Acid Profile in Children with Phenylketonuria
por: Daly, Anne, et al.
Publicado: (2020)

Dietetic Management of Adults with Phenylketonuria (PKU) in the UK: A Care Consensus Document
por: Robertson, Louise, et al.
Publicado: (2022)

The Use of Glycomacropeptide in Patients with Phenylketonuria: A Systematic Review and Meta-Analysis
por: Pena, Maria João, et al.
Publicado: (2018)

Uniformity of Food Protein Interpretation Amongst Dietitians for Patients with Phenylketonuria (PKU): 2020 UK National Consensus Statements
por: Evans, Sharon, et al.
Publicado: (2020)

Influence of Glycomacropeptide on Rehydration Characteristics of Micellar Casein Concentrate Powder
por: Panthi, Ram R., et al.
Publicado: (2021)

Growth, Protein and Energy Intake in Children with PKU Taking a Weaning Protein Substitute in the First Two Years of Life: A Case-Control Study
por: Evans, Sharon, et al.
Publicado: (2019)

PKU dietary handbook to accompany PKU guidelines
por: MacDonald, A., et al.
Publicado: (2020)

Correction to: PKU dietary handbook to accompany PKU guidelines
por: MacDonald, A., et al.
Publicado: (2020)

Living with Phenylketonuria: Lessons from the PKU community
por: Ford, Suzanne, et al.
Publicado: (2018)

Comparison of Glycomacropeptide with Phenylalanine Free-Synthetic Amino Acids in Test Meals to PKU Patients: No Significant Differences in Biomarkers, Including Plasma Phe Levels
por: Ahring, Kirsten K., et al.
Publicado: (2018)

The Impact of the Quality of Nutrition and Lifestyle in the Reproductive Years of Women with PKU on the Long-Term Health of Their Children
por: Gama, Maria Inês, et al.
Publicado: (2022)

Adult PKU Clinics in the UK—Users’ Experiences and Perspectives
por: Ilgaz, Fatma, et al.
Publicado: (2023)

Moving through adulthood: The lived experience of Irish adults with PKU
por: O'Shea, Mary-Ellen, et al.
Publicado: (2022)

Unveiling the Metabolic Effects of Glycomacropeptide
por: Pena, Maria João, et al.
Publicado: (2021)

Dietary Management, Clinical Status and Outcome of Patients with Citrin Deficiency in the UK
por: Pinto, Alex, et al.
Publicado: (2020)

Patient’s thoughts and expectations about centres of expertise for PKU
por: van Wegberg, A. M. J., et al.
Publicado: (2021)

Dietary management of maternal phenylketonuria with glycomacropeptide and amino acids supplements: A case report
por: Pinto, A., et al.
Publicado: (2017)

Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective
por: Pena, Maria João, et al.
Publicado: (2021)

The Use of Glycomacropeptide in Dietary Management of Phenylketonuria
por: Zaki, Osama K., et al.
Publicado: (2016)

Dietary Liberalization in Tetrahydrobiopterin-Treated PKU Patients: Does It Improve Outcomes?
por: Evers, Roeland A. F., et al.
Publicado: (2022)

Cannot write session to /tmp/vufind_sessions/sess_h5fvv6n5ef74rplrdtuk6oausq