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Impact on Diet Quality and Burden of Care in Sapropterin Dihydrochloride Use in Children with Phenylketonuria: A 6 Month Follow-Up Report

Introduction: In phenylketonuria (PKU) changes in dietary patterns and behaviors in sapropterin-responsive populations have not been widely reported. We aimed to assess changes in food quality, mental health and burden of care in a paediatric PKU sapropterin-responsive cohort. Methods: In an observa...

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Detalles Bibliográficos
Autores principales:	Gama, Maria Inês, Daly, Anne, Ashmore, Catherine, Evans, Sharon, Moreira-Rosário, André, Rocha, Júlio César, MacDonald, Anita
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10459538/ https://www.ncbi.nlm.nih.gov/pubmed/37630793 http://dx.doi.org/10.3390/nu15163603

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