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Cerebellar structural, astrocytic, and neuronal abnormalities in the SMNΔ7 mouse model of spinal muscular atrophy
Spinalmuscular atrophy (SMA) is a neuromuscular disease that affects as many as 1 in 6000 individuals at birth, making it the leading genetic cause of infant mortality. A growing number of studies indicate that SMA is a multi‐system disease. The cerebellum has received little attention even though i...
Autores principales: | Cottam, Nicholas C., Bamfo, Tiffany, Harrington, Melissa A., Charvet, Christine J., Hekmatyar, Khan, Tulin, Nikita, Sun, Jianli |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10467044/ https://www.ncbi.nlm.nih.gov/pubmed/37218083 http://dx.doi.org/10.1111/bpa.13162 |
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