Cargando…
Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up
Sclerosing/spindle cell rhabdomyosarcoma (s-scRMS) is a rare variant of striated muscle tumours. It has been recognised as an individual entity, the fourth subtype of rhabdomyosarcoma in the latest WHO classification. In the paediatric population, it occurs more commonly in the paratesticular area,...
Autores principales: | , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Cureus
2023
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10473976/ https://www.ncbi.nlm.nih.gov/pubmed/37664329 http://dx.doi.org/10.7759/cureus.42869 |
_version_ | 1785100390776176640 |
---|---|
author | Othman, Homihidayah Mohamed Haflah, Nor Hazla Sani, Mohamed H Wan Ismail, Wan Faisham Kesu Belani, Levin |
author_facet | Othman, Homihidayah Mohamed Haflah, Nor Hazla Sani, Mohamed H Wan Ismail, Wan Faisham Kesu Belani, Levin |
author_sort | Othman, Homihidayah |
collection | PubMed |
description | Sclerosing/spindle cell rhabdomyosarcoma (s-scRMS) is a rare variant of striated muscle tumours. It has been recognised as an individual entity, the fourth subtype of rhabdomyosarcoma in the latest WHO classification. In the paediatric population, it occurs more commonly in the paratesticular area, whereas in adults, it occurs more commonly in the head and neck region. It has distinctive characteristics in terms of its histopathological and immunochemistry findings, which help in accurate diagnosis. The mainstay of treatment is a multimodal approach, i.e., surgery, chemotherapy, and radiation therapy. However, no standard care is still being established internationally for adult cases. In adults, this tumour has a poorer prognosis as compared to children. We describe a patient with s-scRMS of the lower limb who has undergone wide local resection of the tumour with surgical reconstruction of the distal tibiofibular joint with autograft and its two-year outcome. |
format | Online Article Text |
id | pubmed-10473976 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Cureus |
record_format | MEDLINE/PubMed |
spelling | pubmed-104739762023-09-03 Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up Othman, Homihidayah Mohamed Haflah, Nor Hazla Sani, Mohamed H Wan Ismail, Wan Faisham Kesu Belani, Levin Cureus Oncology Sclerosing/spindle cell rhabdomyosarcoma (s-scRMS) is a rare variant of striated muscle tumours. It has been recognised as an individual entity, the fourth subtype of rhabdomyosarcoma in the latest WHO classification. In the paediatric population, it occurs more commonly in the paratesticular area, whereas in adults, it occurs more commonly in the head and neck region. It has distinctive characteristics in terms of its histopathological and immunochemistry findings, which help in accurate diagnosis. The mainstay of treatment is a multimodal approach, i.e., surgery, chemotherapy, and radiation therapy. However, no standard care is still being established internationally for adult cases. In adults, this tumour has a poorer prognosis as compared to children. We describe a patient with s-scRMS of the lower limb who has undergone wide local resection of the tumour with surgical reconstruction of the distal tibiofibular joint with autograft and its two-year outcome. Cureus 2023-08-02 /pmc/articles/PMC10473976/ /pubmed/37664329 http://dx.doi.org/10.7759/cureus.42869 Text en Copyright © 2023, Othman et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Oncology Othman, Homihidayah Mohamed Haflah, Nor Hazla Sani, Mohamed H Wan Ismail, Wan Faisham Kesu Belani, Levin Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up |
title | Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up |
title_full | Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up |
title_fullStr | Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up |
title_full_unstemmed | Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up |
title_short | Distal Tibiofibular Joint Reconstruction Using Autograft in a Rare Case of Lower Limb Sclerosing/Spindle Cell Rhabdomyosarcoma: A Two-Year Follow-Up |
title_sort | distal tibiofibular joint reconstruction using autograft in a rare case of lower limb sclerosing/spindle cell rhabdomyosarcoma: a two-year follow-up |
topic | Oncology |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10473976/ https://www.ncbi.nlm.nih.gov/pubmed/37664329 http://dx.doi.org/10.7759/cureus.42869 |
work_keys_str_mv | AT othmanhomihidayah distaltibiofibularjointreconstructionusingautograftinararecaseoflowerlimbsclerosingspindlecellrhabdomyosarcomaatwoyearfollowup AT mohamedhaflahnorhazla distaltibiofibularjointreconstructionusingautograftinararecaseoflowerlimbsclerosingspindlecellrhabdomyosarcomaatwoyearfollowup AT sanimohamedh distaltibiofibularjointreconstructionusingautograftinararecaseoflowerlimbsclerosingspindlecellrhabdomyosarcomaatwoyearfollowup AT wanismailwanfaisham distaltibiofibularjointreconstructionusingautograftinararecaseoflowerlimbsclerosingspindlecellrhabdomyosarcomaatwoyearfollowup AT kesubelanilevin distaltibiofibularjointreconstructionusingautograftinararecaseoflowerlimbsclerosingspindlecellrhabdomyosarcomaatwoyearfollowup |