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Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report
Moebius syndrome (MBS) is a rare congenital nonprogressive neuromuscular disorder characterized by partial or complete, unilateral or bilateral paralysis of the facial (VII) and abducens (VI) cranial nerves (CNs). In this syndrome bilateral facial palsy may occur with the involvement of VII CN and i...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Jaypee Brothers Medical Publishers
2023
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10474396/ https://www.ncbi.nlm.nih.gov/pubmed/37663216 http://dx.doi.org/10.5005/jp-journals-10005-2626 |
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author | Mittal, Meenu Kumar, Ashok Chopra, Radhika Tomar, Prashant |
author_facet | Mittal, Meenu Kumar, Ashok Chopra, Radhika Tomar, Prashant |
author_sort | Mittal, Meenu |
collection | PubMed |
description | Moebius syndrome (MBS) is a rare congenital nonprogressive neuromuscular disorder characterized by partial or complete, unilateral or bilateral paralysis of the facial (VII) and abducens (VI) cranial nerves (CNs). In this syndrome bilateral facial palsy may occur with the involvement of VII CN and impaired eye movements can be there because of the involvement of VI CN. It can also be associated with other CN palsies, orofacial anomalies, and limb defects. MBS is diagnosed exclusively on the basis of clinical criteria, although causative genetic patterns are being documented in recent studies. The present case report describes the dental management of a 5-year-old child diagnosed with MBS. The child presented with the abnormal shape of legs, incomplete eye closure during sleep, inability to smile, lingual hypoplasia, microstomia, and hypoplastic teeth among other dental-skeletal abnormalities, and a clinical diagnosis of MBS was made. HOW TO CITE THIS ARTICLE: Mittal M, Kumar A, Chopra R, et al. Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report. Int J Clin Pediatr Dent 2023;16(S-1):S109–S112. |
format | Online Article Text |
id | pubmed-10474396 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Jaypee Brothers Medical Publishers |
record_format | MEDLINE/PubMed |
spelling | pubmed-104743962023-09-03 Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report Mittal, Meenu Kumar, Ashok Chopra, Radhika Tomar, Prashant Int J Clin Pediatr Dent Case Report Moebius syndrome (MBS) is a rare congenital nonprogressive neuromuscular disorder characterized by partial or complete, unilateral or bilateral paralysis of the facial (VII) and abducens (VI) cranial nerves (CNs). In this syndrome bilateral facial palsy may occur with the involvement of VII CN and impaired eye movements can be there because of the involvement of VI CN. It can also be associated with other CN palsies, orofacial anomalies, and limb defects. MBS is diagnosed exclusively on the basis of clinical criteria, although causative genetic patterns are being documented in recent studies. The present case report describes the dental management of a 5-year-old child diagnosed with MBS. The child presented with the abnormal shape of legs, incomplete eye closure during sleep, inability to smile, lingual hypoplasia, microstomia, and hypoplastic teeth among other dental-skeletal abnormalities, and a clinical diagnosis of MBS was made. HOW TO CITE THIS ARTICLE: Mittal M, Kumar A, Chopra R, et al. Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report. Int J Clin Pediatr Dent 2023;16(S-1):S109–S112. Jaypee Brothers Medical Publishers 2023-08 /pmc/articles/PMC10474396/ /pubmed/37663216 http://dx.doi.org/10.5005/jp-journals-10005-2626 Text en Copyright © 2023; The Author(s). https://creativecommons.org/licenses/by-nc/4.0/© The Author(s). 2023 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (https://creativecommons.org/licenses/by-nc/4.0/), which permits unrestricted use, distribution, and non-commercial reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/ (https://creativecommons.org/publicdomain/zero/1.0/) ) applies to the data made available in this article, unless otherwise stated. |
spellingShingle | Case Report Mittal, Meenu Kumar, Ashok Chopra, Radhika Tomar, Prashant Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report |
title | Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report |
title_full | Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report |
title_fullStr | Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report |
title_full_unstemmed | Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report |
title_short | Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report |
title_sort | diagnosis and dental management of a child with moebius syndrome: a case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10474396/ https://www.ncbi.nlm.nih.gov/pubmed/37663216 http://dx.doi.org/10.5005/jp-journals-10005-2626 |
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