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Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report
Kasabach‐Merritt phenomenon (KMP) is a rare condition that is associated with two rare vascular tumours: Kapossiform haemangioendothelioma (KHE) and tufted angioma (TA). A 2‐year‐old girl presented to our emergency room with a haemangioma and respiratory distress. The patient had a violaceous, palpa...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley & Sons, Ltd
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10477463/ https://www.ncbi.nlm.nih.gov/pubmed/37675387 http://dx.doi.org/10.1002/rcr2.1206 |
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author | Cesilia, Citra Ridar, Elmi Hatta, Hariadi Makmur, Andreas Wiwit Ade, FW Melinda Nataprawira, Heda |
author_facet | Cesilia, Citra Ridar, Elmi Hatta, Hariadi Makmur, Andreas Wiwit Ade, FW Melinda Nataprawira, Heda |
author_sort | Cesilia, Citra |
collection | PubMed |
description | Kasabach‐Merritt phenomenon (KMP) is a rare condition that is associated with two rare vascular tumours: Kapossiform haemangioendothelioma (KHE) and tufted angioma (TA). A 2‐year‐old girl presented to our emergency room with a haemangioma and respiratory distress. The patient had a violaceous, palpable mass in the right upper chest since she was 5 months old. Severe anaemia, thrombocytopenia, coagulopathy, and hypofibrinogenemia were found. Chest x‐ray revealed massive pleural effusion in the right hemithorax. Chest computed tomography (CT) scanning revealed right pleural effusion, multiple destructions of bilateral ribs and multiple osteopenia of thoracic vertebrae. Chest CT angiography revealed a vascular mass in the sternum region. Based on clinical, laboratory and imaging findings, the diagnosis of KMP was established. Clinical, consumptive coagulopathy and thrombocytopenia were resolved by prednisone (3 mg/kg/day) and vincristine (1 mg/body surface area in m(2)/week) as an adjunct. Unfortunately, she had spontaneous rebleeding and died before the biopsy was done. |
format | Online Article Text |
id | pubmed-10477463 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | John Wiley & Sons, Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-104774632023-09-06 Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report Cesilia, Citra Ridar, Elmi Hatta, Hariadi Makmur, Andreas Wiwit Ade, FW Melinda Nataprawira, Heda Respirol Case Rep Case Reports Kasabach‐Merritt phenomenon (KMP) is a rare condition that is associated with two rare vascular tumours: Kapossiform haemangioendothelioma (KHE) and tufted angioma (TA). A 2‐year‐old girl presented to our emergency room with a haemangioma and respiratory distress. The patient had a violaceous, palpable mass in the right upper chest since she was 5 months old. Severe anaemia, thrombocytopenia, coagulopathy, and hypofibrinogenemia were found. Chest x‐ray revealed massive pleural effusion in the right hemithorax. Chest computed tomography (CT) scanning revealed right pleural effusion, multiple destructions of bilateral ribs and multiple osteopenia of thoracic vertebrae. Chest CT angiography revealed a vascular mass in the sternum region. Based on clinical, laboratory and imaging findings, the diagnosis of KMP was established. Clinical, consumptive coagulopathy and thrombocytopenia were resolved by prednisone (3 mg/kg/day) and vincristine (1 mg/body surface area in m(2)/week) as an adjunct. Unfortunately, she had spontaneous rebleeding and died before the biopsy was done. John Wiley & Sons, Ltd 2023-09-04 /pmc/articles/PMC10477463/ /pubmed/37675387 http://dx.doi.org/10.1002/rcr2.1206 Text en © 2023 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology. https://creativecommons.org/licenses/by/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Reports Cesilia, Citra Ridar, Elmi Hatta, Hariadi Makmur, Andreas Wiwit Ade, FW Melinda Nataprawira, Heda Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report |
title | Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report |
title_full | Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report |
title_fullStr | Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report |
title_full_unstemmed | Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report |
title_short | Spontaneous haemothorax as a complication of Kassabach‐Merritt phenomenon (KMP) in a‐2‐years old female child: A case report |
title_sort | spontaneous haemothorax as a complication of kassabach‐merritt phenomenon (kmp) in a‐2‐years old female child: a case report |
topic | Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10477463/ https://www.ncbi.nlm.nih.gov/pubmed/37675387 http://dx.doi.org/10.1002/rcr2.1206 |
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