A Massive Craniofacial Polyostotic Fibrous Dysplasia of Midface – A Rare Case Report

RATIONALE: Fibrous dysplasia (FD) is a fibro-osseous lesion of the osseous structures of the body. With an incidence of 1:4000–1:10,000, it seems to be a rare disease. Polyostotic craniofacial fibrous dysplasia involves the skull base bones and facial bones. PATIENT CONCERNS: The patient complained of a huge swelling over the right side of her face for the past 12 years. DIAGNOSIS: Based on clinical, radiological and histopathological findings, the swelling was diagnosed as polyostotic craniofacial FD. TREATMENT: Swelling over the right side of the midface around 6 cm × 5 cm involving right maxilla, zygoma, floor of orbit, lateral side of nose (pyriform aperture) and skull base bones. Since the patient had no functional deficit, we opted for surgical recontouring. OUTCOMES: The patient was satisfied with post-operative results. TAKE-AWAY LESSONS: In huge asymptomatic facial deformity, rather than going for resection, we can remove bone in a piecemeal manner followed by recontouring.