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Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient

Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue sarcoma that originates from peripheral nerves or from cells associated with the nerve sheath. We report the case of a 30yearold male patient with a history of neurofibromatosis type I (NF-1) and a MPNST located in the lumbar regi...

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Autores principales: Paparella, Maria Teresa, Eusebi, Laura, Mazzucchelli, Roberta, Guglielmi, Giuseppe
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Mattioli 1885 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10510982/
https://www.ncbi.nlm.nih.gov/pubmed/35420598
http://dx.doi.org/10.23750/abm.v93iS1.12360
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author Paparella, Maria Teresa
Eusebi, Laura
Mazzucchelli, Roberta
Guglielmi, Giuseppe
author_facet Paparella, Maria Teresa
Eusebi, Laura
Mazzucchelli, Roberta
Guglielmi, Giuseppe
author_sort Paparella, Maria Teresa
collection PubMed
description Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue sarcoma that originates from peripheral nerves or from cells associated with the nerve sheath. We report the case of a 30yearold male patient with a history of neurofibromatosis type I (NF-1) and a MPNST located in the lumbar region. The mass was resecated but surgical margins weren’t clear. Recurrence of disease was observed after a few months. A close monitoring of subjects with NF-1 is crucial to diagnose MPNST at an earlier stage and allow a complete surgical resection (www.actabiomedica.it).
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spelling pubmed-105109822023-09-21 Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient Paparella, Maria Teresa Eusebi, Laura Mazzucchelli, Roberta Guglielmi, Giuseppe Acta Biomed Case Report Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue sarcoma that originates from peripheral nerves or from cells associated with the nerve sheath. We report the case of a 30yearold male patient with a history of neurofibromatosis type I (NF-1) and a MPNST located in the lumbar region. The mass was resecated but surgical margins weren’t clear. Recurrence of disease was observed after a few months. A close monitoring of subjects with NF-1 is crucial to diagnose MPNST at an earlier stage and allow a complete surgical resection (www.actabiomedica.it). Mattioli 1885 2022 2022-12-07 /pmc/articles/PMC10510982/ /pubmed/35420598 http://dx.doi.org/10.23750/abm.v93iS1.12360 Text en Copyright: © 2022 ACTA BIO MEDICA SOCIETY OF MEDICINE AND NATURAL SCIENCES OF PARMA https://creativecommons.org/licenses/by-nc-sa/4.0/This work is licensed under a Creative Commons Attribution 4.0 International License
spellingShingle Case Report
Paparella, Maria Teresa
Eusebi, Laura
Mazzucchelli, Roberta
Guglielmi, Giuseppe
Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
title Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
title_full Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
title_fullStr Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
title_full_unstemmed Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
title_short Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
title_sort lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10510982/
https://www.ncbi.nlm.nih.gov/pubmed/35420598
http://dx.doi.org/10.23750/abm.v93iS1.12360
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