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Biofabrication of an in-vitro bone model for Gaucher disease
Gaucher disease (GD), the most prevalent lysosomal disorder, is caused by GBA1 gene mutations, leading to deficiency of glucocerebrosidase, and accumulation of glycosphingolipids in cells of the mononuclear phagocyte system. While skeletal diseases are the leading cause of morbidity and reduced qual...
Autores principales: | Banerjee, Dishary, Ivanova, Margarita M, Celik, Nazmiye, Kim, Myoung Hwan, Derman, Irem Deniz, Limgala, Renuka Pudi, Ozbolat, Ibrahim T, Goker-Alpan, Ozlem |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
IOP Publishing
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10515412/ https://www.ncbi.nlm.nih.gov/pubmed/37703870 http://dx.doi.org/10.1088/1758-5090/acf95a |
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