The Management of Pyromelic Polymelia in a Low-resource Setting: A Case Report

INTRODUCTION: Polymelia is the presence of supernumerary limbs attached to a segment of the body. It occurs in about 6/10,000 live births with 1.1/10,000 cases involving the lower limbs. It has a heterogeneous pathogenesis including incomplete separation of monozygotic twins. CASE REPORT: A 5-month-...

Descripción completa

Detalles Bibliográficos
Autores principales: Konadu-Yeboah, Dominic, Sobotie, Johnny, Boadi, Samuel Twene, Akomea-Agyin, Ebenezer, Davor, Anthony, Okrah, Helena
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Indian Orthopaedic Research Group 2023
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10519300/
https://www.ncbi.nlm.nih.gov/pubmed/37753130
http://dx.doi.org/10.13107/jocr.2023.v13.i09.3876
Descripción
Sumario:INTRODUCTION: Polymelia is the presence of supernumerary limbs attached to a segment of the body. It occurs in about 6/10,000 live births with 1.1/10,000 cases involving the lower limbs. It has a heterogeneous pathogenesis including incomplete separation of monozygotic twins. CASE REPORT: A 5-month-old baby with polymelia associated with ectopic right kidney, anorectal agenesis with a rectovaginal fistula, and right corneal opacity, delivered through cesarean section at 37 weeks, 3-day gestation to a 38-year-old mother. There were no known predisposing factors. CONCLUSION: In the management of polymelia, a thorough clinical and radiological assessment to identify additional anomalies is critical, and early surgical intervention is safe and optimizes survival.

Ejemplares similares