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Femoral Structure and Biomechanical Characteristics in Sanfilippo Syndrome Type-B Mice

Sanfilippo syndrome Type-B, also known as mucopolysaccharidosis IIIB (MPS IIIB), accounts for approximately one-third of all Sanfilippo syndrome patients and is characterized by a similar natural history as Type-A. Patients suffer from developmental regression, bone malformation, organomegaly, GI di...

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Detalles Bibliográficos
Autores principales:	Ashby, Frederick James, Castillo, Evelyn J., Ludwig, Yan, Andraka, Natalia K., Chen, Cong, Jamieson, Julia C., Kabbej, Nadia, Sommerville, John D., Aguirre, Jose I., Heldermon, Coy D.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10530914/ https://www.ncbi.nlm.nih.gov/pubmed/37762291 http://dx.doi.org/10.3390/ijms241813988

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