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Clinicopathologic Features, Genetics, Treatment, and Long-Term Outcomes in Japanese Children and Young Adults with Benign Recurrent Intrahepatic Cholestasis: A Multicenter Study
Background: Few reports of benign recurrent intrahepatic cholestasis (BRIC) have focused on East Asian patients. We describe the clinicopathologic features, genetics, treatment, and outcomes in Japanese BRIC patients. Methods: We recruited patients with BRIC type 1 (BRIC-1) or 2 (BRIC-2) treated at...
Autores principales: | Kato, Ken, Umetsu, Shuichiro, Togawa, Takao, Ito, Koichi, Kawabata, Takayoshi, Arinaga-Hino, Teruko, Tsumura, Naoya, Yasuda, Ryosuke, Mihara, Yutaro, Kusano, Hironori, Ito, Shogo, Imagawa, Kazuo, Hayashi, Hisamitsu, Inui, Ayano, Yamashita, Yushiro, Mizuochi, Tatsuki |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10532077/ https://www.ncbi.nlm.nih.gov/pubmed/37762919 http://dx.doi.org/10.3390/jcm12185979 |
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