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Expert Consensus on the Long-Term Effectiveness of Medical Nutrition Therapy and Its Impact on the Outcomes of Adults with Phenylketonuria

Many adults with phenylketonuria (PKU) rely on medical nutrition therapy (MNT; low phenylalanine (Phe) diet with protein substitutes/medical foods) to maintain blood Phe concentrations within recommended ranges and prevent PKU-associated comorbidities. Despite disease detection through newborn scree...

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Detalles Bibliográficos
Autores principales:	Rocha, Júlio César, Ahring, Kirsten K., Bausell, Heather, Bilder, Deborah A., Harding, Cary O., Inwood, Anita, Longo, Nicola, Muntau, Ania C., Pessoa, André L. Santos, Rohr, Fran, Sivri, Serap, Hermida, Álvaro
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10536918/ https://www.ncbi.nlm.nih.gov/pubmed/37764724 http://dx.doi.org/10.3390/nu15183940

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