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Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review

Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography sh...

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Detalles Bibliográficos
Autores principales: Akkuzu, Gamze, Özgür, Duygu Sevinç, Karaalioğlu, Bilgin, Mutlu, Melek Yalçın, Yıldırım, Fatih, Erdoğan, Mustafa, İnce, Burak, Bes, Cemal
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Mesut Onat 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10544313/
https://www.ncbi.nlm.nih.gov/pubmed/37470383
http://dx.doi.org/10.5152/eurjrheum.2023.22043
Descripción
Sumario:Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography showed occlusion of the right subclavian artery at the level of the thoracic outlet and reverse flow in the right vertebral artery consistent with subclavian steal syndrome. In addition, partial narrowing was noted in the left renal artery. The distribution of arterial involvement resembled Takayasu’s arteritis, although the presence of mucocutaneous lesions, male gender, history of deep vein thrombosis, and HLA-B51 positivity favored a diagnosis of vasculo-Behçet’s syndrome. We treated the patient with methylprednisolone and cyclophosphamide. After the regression of vascular inflammation with immunosuppressive therapy, stenting was performed in the left renal artery.