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Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review

Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography sh...

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Autores principales: Akkuzu, Gamze, Özgür, Duygu Sevinç, Karaalioğlu, Bilgin, Mutlu, Melek Yalçın, Yıldırım, Fatih, Erdoğan, Mustafa, İnce, Burak, Bes, Cemal
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Mesut Onat 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10544313/
https://www.ncbi.nlm.nih.gov/pubmed/37470383
http://dx.doi.org/10.5152/eurjrheum.2023.22043
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author Akkuzu, Gamze
Özgür, Duygu Sevinç
Karaalioğlu, Bilgin
Mutlu, Melek Yalçın
Yıldırım, Fatih
Erdoğan, Mustafa
İnce, Burak
Bes, Cemal
author_facet Akkuzu, Gamze
Özgür, Duygu Sevinç
Karaalioğlu, Bilgin
Mutlu, Melek Yalçın
Yıldırım, Fatih
Erdoğan, Mustafa
İnce, Burak
Bes, Cemal
author_sort Akkuzu, Gamze
collection PubMed
description Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography showed occlusion of the right subclavian artery at the level of the thoracic outlet and reverse flow in the right vertebral artery consistent with subclavian steal syndrome. In addition, partial narrowing was noted in the left renal artery. The distribution of arterial involvement resembled Takayasu’s arteritis, although the presence of mucocutaneous lesions, male gender, history of deep vein thrombosis, and HLA-B51 positivity favored a diagnosis of vasculo-Behçet’s syndrome. We treated the patient with methylprednisolone and cyclophosphamide. After the regression of vascular inflammation with immunosuppressive therapy, stenting was performed in the left renal artery.
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spelling pubmed-105443132023-10-03 Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review Akkuzu, Gamze Özgür, Duygu Sevinç Karaalioğlu, Bilgin Mutlu, Melek Yalçın Yıldırım, Fatih Erdoğan, Mustafa İnce, Burak Bes, Cemal Eur J Rheumatol Case-Based Review Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography showed occlusion of the right subclavian artery at the level of the thoracic outlet and reverse flow in the right vertebral artery consistent with subclavian steal syndrome. In addition, partial narrowing was noted in the left renal artery. The distribution of arterial involvement resembled Takayasu’s arteritis, although the presence of mucocutaneous lesions, male gender, history of deep vein thrombosis, and HLA-B51 positivity favored a diagnosis of vasculo-Behçet’s syndrome. We treated the patient with methylprednisolone and cyclophosphamide. After the regression of vascular inflammation with immunosuppressive therapy, stenting was performed in the left renal artery. Mesut Onat 2023-04-01 /pmc/articles/PMC10544313/ /pubmed/37470383 http://dx.doi.org/10.5152/eurjrheum.2023.22043 Text en 2023 authors https://creativecommons.org/licenses/by-nc/4.0/ Content of this journal is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License. (https://creativecommons.org/licenses/by-nc/4.0/)
spellingShingle Case-Based Review
Akkuzu, Gamze
Özgür, Duygu Sevinç
Karaalioğlu, Bilgin
Mutlu, Melek Yalçın
Yıldırım, Fatih
Erdoğan, Mustafa
İnce, Burak
Bes, Cemal
Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
title Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
title_full Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
title_fullStr Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
title_full_unstemmed Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
title_short Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
title_sort bahcet’s syndrome resembling takayasu’s arteritis with the distribution of arterial involvement: a case report and literature review
topic Case-Based Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10544313/
https://www.ncbi.nlm.nih.gov/pubmed/37470383
http://dx.doi.org/10.5152/eurjrheum.2023.22043
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