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Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review
Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography sh...
Autores principales: | , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Mesut Onat
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10544313/ https://www.ncbi.nlm.nih.gov/pubmed/37470383 http://dx.doi.org/10.5152/eurjrheum.2023.22043 |
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author | Akkuzu, Gamze Özgür, Duygu Sevinç Karaalioğlu, Bilgin Mutlu, Melek Yalçın Yıldırım, Fatih Erdoğan, Mustafa İnce, Burak Bes, Cemal |
author_facet | Akkuzu, Gamze Özgür, Duygu Sevinç Karaalioğlu, Bilgin Mutlu, Melek Yalçın Yıldırım, Fatih Erdoğan, Mustafa İnce, Burak Bes, Cemal |
author_sort | Akkuzu, Gamze |
collection | PubMed |
description | Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography showed occlusion of the right subclavian artery at the level of the thoracic outlet and reverse flow in the right vertebral artery consistent with subclavian steal syndrome. In addition, partial narrowing was noted in the left renal artery. The distribution of arterial involvement resembled Takayasu’s arteritis, although the presence of mucocutaneous lesions, male gender, history of deep vein thrombosis, and HLA-B51 positivity favored a diagnosis of vasculo-Behçet’s syndrome. We treated the patient with methylprednisolone and cyclophosphamide. After the regression of vascular inflammation with immunosuppressive therapy, stenting was performed in the left renal artery. |
format | Online Article Text |
id | pubmed-10544313 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Mesut Onat |
record_format | MEDLINE/PubMed |
spelling | pubmed-105443132023-10-03 Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review Akkuzu, Gamze Özgür, Duygu Sevinç Karaalioğlu, Bilgin Mutlu, Melek Yalçın Yıldırım, Fatih Erdoğan, Mustafa İnce, Burak Bes, Cemal Eur J Rheumatol Case-Based Review Behcet’s syndrome is a variable vessel vasculitis characterized by recurrent oral and genital ulcers with concomitant skin, ocular, neurologic, gastrointestinal, and joint involvement. Herein, we present a patient who was diagnosed with Behcet’s syndrome, which with magnetic resonance angiography showed occlusion of the right subclavian artery at the level of the thoracic outlet and reverse flow in the right vertebral artery consistent with subclavian steal syndrome. In addition, partial narrowing was noted in the left renal artery. The distribution of arterial involvement resembled Takayasu’s arteritis, although the presence of mucocutaneous lesions, male gender, history of deep vein thrombosis, and HLA-B51 positivity favored a diagnosis of vasculo-Behçet’s syndrome. We treated the patient with methylprednisolone and cyclophosphamide. After the regression of vascular inflammation with immunosuppressive therapy, stenting was performed in the left renal artery. Mesut Onat 2023-04-01 /pmc/articles/PMC10544313/ /pubmed/37470383 http://dx.doi.org/10.5152/eurjrheum.2023.22043 Text en 2023 authors https://creativecommons.org/licenses/by-nc/4.0/ Content of this journal is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License. (https://creativecommons.org/licenses/by-nc/4.0/) |
spellingShingle | Case-Based Review Akkuzu, Gamze Özgür, Duygu Sevinç Karaalioğlu, Bilgin Mutlu, Melek Yalçın Yıldırım, Fatih Erdoğan, Mustafa İnce, Burak Bes, Cemal Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review |
title | Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review |
title_full | Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review |
title_fullStr | Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review |
title_full_unstemmed | Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review |
title_short | Bahcet’s Syndrome Resembling Takayasu’s Arteritis with the Distribution of Arterial Involvement: A Case Report and Literature Review |
title_sort | bahcet’s syndrome resembling takayasu’s arteritis with the distribution of arterial involvement: a case report and literature review |
topic | Case-Based Review |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10544313/ https://www.ncbi.nlm.nih.gov/pubmed/37470383 http://dx.doi.org/10.5152/eurjrheum.2023.22043 |
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