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Mitochondrial Dysfunction and Decreased Cytochrome c in Cell and Animal Models of Machado–Joseph Disease

Mitochondrial dysfunction has been described in many neurodegenerative disorders; however, there is less information regarding mitochondrial deficits in Machado–Joseph disease (MJD), a polyglutamine (polyQ) disorder caused by CAG repeat expansion in the ATXN3 gene. In the present study, we character...

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Detalles Bibliográficos
Autores principales:	Almeida, Filipa, Ferreira, Ildete L., Naia, Luana, Marinho, Daniela, Vilaça-Ferreira, Ana Catarina, Costa, Marta D., Duarte-Silva, Sara, Maciel, Patrícia, Rego, A. Cristina
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10571982/ https://www.ncbi.nlm.nih.gov/pubmed/37830611 http://dx.doi.org/10.3390/cells12192397

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