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Outcomes and prognosis of progressive pulmonary fibrosis in patients with antineutrophil cytoplasmic antibody-positive interstitial lung disease

Approximately one-third of fibrosing interstitial lung diseases exhibit progressive pulmonary fibrosis (PPF), a clinicopathological condition distinct yet resembling idiopathic pulmonary fibrosis (IPF). PPF in ANCA-positive ILD (ANCA-ILD) is poorly documented. To clarify incidence, predictors of PPF...

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Detalles Bibliográficos
Autores principales: Sakamoto, Susumu, Suzuki, Aika, Homma, Sakae, Usui, Yusuke, Shimizu, Hiroshige, Sekiya, Muneyuki, Miyoshi, Shion, Nakamura, Yasuhiko, Urabe, Naohisa, Isshiki, Takuma, Kurosaki, Atsuko, Kishi, Kazuma
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group UK 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10582016/
https://www.ncbi.nlm.nih.gov/pubmed/37848575
http://dx.doi.org/10.1038/s41598-023-45027-0

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