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Autophagy increase in Merosin-Deficient Congenital Muscular Dystrophy type 1A

The autophagy process recycles dysfunctional cellular components and protein aggregates by sequestering them in autophagosomes directed to lysosomes for enzymatic degradation. A basal level of autophagy is essential for skeletal muscle maintenance. Increased autophagy occurs in several forms of musc...

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Detalles Bibliográficos
Autores principales:	Mastrapasqua, Mariangela, Rossi, Roberta, De Cosmo, Lucrezia, Resta, Annalisa, Errede, Mariella, Bizzoca, Antonella, Zampatti, Stefania, Resta, Nicoletta, Giardina, Emiliano, Ruggieri, Maddalena, Virgintino, Daniela, Annese, Tiziana, Laforgia, Nicola, Girolamo, Francesco
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	PAGEPress Publications, Pavia, Italy 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10583158/ https://www.ncbi.nlm.nih.gov/pubmed/37522802 http://dx.doi.org/10.4081/ejtm.2023.11501

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