Cargando…

Pulmonary hypertension in hereditary hemorrhagic telangiectasia: A clinical review

Hereditary hemorrhagic telangiectasia (HHT) is a rare autosomal dominant hereditary disorder characterized by recurrent spontaneous epistaxis, mucocutaneous telangiectasias, and solid organ arteriovenous malformations (AVMs). Pulmonary hypertension (PH) is an increasingly recognized complication in...

Descripción completa

Detalles Bibliográficos
Autores principales: Mathavan, Akash, Mathavan, Akshay, Reddy, Renuka, Jones, Kirk, Eagan, Christina, Alnuaimat, Hassan, Ataya, Ali
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10585978/
https://www.ncbi.nlm.nih.gov/pubmed/37868718
http://dx.doi.org/10.1002/pul2.12301