Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome

Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler–Danlos syndrome. Loeys–Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we de...

Descripción completa

Detalles Bibliográficos
Autores principales: Sicim, Hüseyin, Ulucan, Ali Ertan, Yurdakök, Okan, Aydemir, Numan Ali
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2023
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10593284/
https://www.ncbi.nlm.nih.gov/pubmed/37876949
http://dx.doi.org/10.4103/apc.apc_22_23
_version_ 1785124419877732352
author Sicim, Hüseyin
Ulucan, Ali Ertan
Yurdakök, Okan
Aydemir, Numan Ali
author_facet Sicim, Hüseyin
Ulucan, Ali Ertan
Yurdakök, Okan
Aydemir, Numan Ali
author_sort Sicim, Hüseyin
collection PubMed
description Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler–Danlos syndrome. Loeys–Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we describe pediatric Bentall procedure, which we successfully performed to a child with LDS (Type I) with giant ascending aortic enlargement and significant aortic regurgitation.
format Online
Article
Text
id pubmed-10593284
institution National Center for Biotechnology Information
language English
publishDate 2023
publisher Wolters Kluwer - Medknow
record_format MEDLINE/PubMed
spelling pubmed-105932842023-10-24 Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome Sicim, Hüseyin Ulucan, Ali Ertan Yurdakök, Okan Aydemir, Numan Ali Ann Pediatr Cardiol Case Report Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler–Danlos syndrome. Loeys–Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we describe pediatric Bentall procedure, which we successfully performed to a child with LDS (Type I) with giant ascending aortic enlargement and significant aortic regurgitation. Wolters Kluwer - Medknow 2023 2023-09-08 /pmc/articles/PMC10593284/ /pubmed/37876949 http://dx.doi.org/10.4103/apc.apc_22_23 Text en Copyright: © 2023 Annals of Pediatric Cardiology https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Sicim, Hüseyin
Ulucan, Ali Ertan
Yurdakök, Okan
Aydemir, Numan Ali
Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome
title Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome
title_full Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome
title_fullStr Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome
title_full_unstemmed Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome
title_short Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys–Dietz syndrome
title_sort pediatric bentall procedure for giant ascending aortic aneurysm in loeys–dietz syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10593284/
https://www.ncbi.nlm.nih.gov/pubmed/37876949
http://dx.doi.org/10.4103/apc.apc_22_23
work_keys_str_mv AT sicimhuseyin pediatricbentallprocedureforgiantascendingaorticaneurysminloeysdietzsyndrome
AT ulucanaliertan pediatricbentallprocedureforgiantascendingaorticaneurysminloeysdietzsyndrome
AT yurdakokokan pediatricbentallprocedureforgiantascendingaorticaneurysminloeysdietzsyndrome
AT aydemirnumanali pediatricbentallprocedureforgiantascendingaorticaneurysminloeysdietzsyndrome

Ejemplares similares