Intracranial lipoma with extra cranial subcutaneous component with a midline bony defect and persistent falcine sinus

Intracranial lipomas are only 0.06–0.46% of intracranial lesions, forming a rare type of congenital malformation. Interhemispheric lipoma associated with subcutaneous component is extremely rare. They are usually asymptomatic, but may also present with seizures, raised intracranial pressure, dementia, hemiparesis, persistent headaches, psychomotor retardation and cranial nerve defects. These are associated with vascular, bone, tentorial and other abnormalities. MR examination must be considered to evaluate for a possibility of intracranial component and to rule out other anomalies. Here, we present features of a rare presentation of intracranial lipoma.