Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices

We report the case of a female who was cured of hemorrhagic esophageal varices caused by paroxysmal nocturnal hemoglobinuria (PNH) through transjugular intrahepatic portosystemic shunt (TIPS) treatment. PNH complicated by portal vein and visceral veins thrombosis without hepatic veins is extremely r...

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Autores principales: Du, Runsen, Zheng, Lihua, Liu, Peng, Zhao, Yaheng, Yang, Yan, Zhang, Lei, Zhao, Zengren
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Medicine
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10634371/
https://www.ncbi.nlm.nih.gov/pubmed/37954556
http://dx.doi.org/10.3389/fmed.2023.1276030
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author Du, Runsen
Zheng, Lihua
Liu, Peng
Zhao, Yaheng
Yang, Yan
Zhang, Lei
Zhao, Zengren
author_facet Du, Runsen
Zheng, Lihua
Liu, Peng
Zhao, Yaheng
Yang, Yan
Zhang, Lei
Zhao, Zengren
author_sort Du, Runsen
collection PubMed
description We report the case of a female who was cured of hemorrhagic esophageal varices caused by paroxysmal nocturnal hemoglobinuria (PNH) through transjugular intrahepatic portosystemic shunt (TIPS) treatment. PNH complicated by portal vein and visceral veins thrombosis without hepatic veins is extremely rare, and as such, it is easy to incorrectly treat due to lack of awareness. Hemorrhagic esophageal varices due to PNH with PVT have been reported in one case in 1974, and here, we report the second.
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spelling pubmed-106343712023-11-10 Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices Du, Runsen Zheng, Lihua Liu, Peng Zhao, Yaheng Yang, Yan Zhang, Lei Zhao, Zengren Front Med (Lausanne) Medicine We report the case of a female who was cured of hemorrhagic esophageal varices caused by paroxysmal nocturnal hemoglobinuria (PNH) through transjugular intrahepatic portosystemic shunt (TIPS) treatment. PNH complicated by portal vein and visceral veins thrombosis without hepatic veins is extremely rare, and as such, it is easy to incorrectly treat due to lack of awareness. Hemorrhagic esophageal varices due to PNH with PVT have been reported in one case in 1974, and here, we report the second. Frontiers Media S.A. 2023-10-25 /pmc/articles/PMC10634371/ /pubmed/37954556 http://dx.doi.org/10.3389/fmed.2023.1276030 Text en Copyright © 2023 Du, Zheng, Liu, Zhao, Yang, Zhang and Zhao. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Medicine
Du, Runsen
Zheng, Lihua
Liu, Peng
Zhao, Yaheng
Yang, Yan
Zhang, Lei
Zhao, Zengren
Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
title Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
title_full Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
title_fullStr Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
title_full_unstemmed Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
title_short Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
title_sort case report: paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices
topic Medicine
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10634371/
https://www.ncbi.nlm.nih.gov/pubmed/37954556
http://dx.doi.org/10.3389/fmed.2023.1276030
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