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Predictors of 6-year event-free survival in Alagille syndrome patients treated with maralixibat, an ileal bile acid transporter inhibitor

BACKGROUND AND AIMS: Refractory pruritus and other complications of cholestasis are indications for liver transplantation (LT) in patients with Alagille syndrome (ALGS). We evaluated predictors of event-free survival and transplant-free survival in patients with ALGS treated with maralixibat (MRX),...

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Detalles Bibliográficos
Autores principales:	Sokol, Ronald J., Gonzales, Emmanuel M., Kamath, Binita M., Baker, Alastair, Vig, Pamela, Mogul, Douglas B., Garner, Will, Hansen, Bettina E., Jacquemin, Emmanuel, Thompson, Richard J.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Lippincott Williams & Wilkins 2023
Materias:	Original Articles: Immune-Mediated Diseases, DILI, and Biliary Tract Disease
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10653287/ https://www.ncbi.nlm.nih.gov/pubmed/37278241 http://dx.doi.org/10.1097/HEP.0000000000000502

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