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Arrhythmogenic Cardiomyopathy: from Preclinical Models to Genotype–phenotype Correlation and Pathophysiology

Arrhythmogenic cardiomyopathy (ACM) is a hereditary myocardial disease characterized by the replacement of the ventricular myocardium with fibrous fatty deposits. ACM is usually inherited in an autosomal dominant pattern with variable penetrance and expressivity, which is mainly related to ventricul...

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Detalles Bibliográficos
Autores principales:	Fan, Xuehui, Yang, Guoqiang, Duru, Firat, Grilli, Maurizio, Akin, Ibrahim, Zhou, Xiaobo, Saguner, Ardan Muammer, EI-Battrawy, Ibrahim
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Springer US 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10661732/ https://www.ncbi.nlm.nih.gov/pubmed/37731079 http://dx.doi.org/10.1007/s12015-023-10615-0

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