Three-dimensional echocardiographic left ventricular strain analysis in Fabry disease: correlation with heart failure severity, myocardial scar, and impact on long-term prognosis

AIMS: Fabry disease (FD) is a multisystemic lysosomal storage disorder caused by a defect in the alpha-galactosidase A gene that manifests as a phenocopy of hypertrophic cardiomyopathy. We assessed the echocardiographic 3D left ventricular (LV) strain of patients with FD in relation to heart failure...

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Detalles Bibliográficos
Autores principales: Marek, Josef, Chocholová, Barbora, Rob, Daniel, Paleček, Tomáš, Mašek, Martin, Dostálová, Gabriela, Linhart, Aleš
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2023
Materias:
Original Paper
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10667034/
https://www.ncbi.nlm.nih.gov/pubmed/37309820
http://dx.doi.org/10.1093/ehjci/jead121

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10667034/
https://www.ncbi.nlm.nih.gov/pubmed/37309820
http://dx.doi.org/10.1093/ehjci/jead121

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